Linear morphea in saber coup: about a case

Linear morphea in coup de sabre is a dermatological entity characterized by progressive, sclerosing inflammation of the skin tissue in the frontal region and on the scalp. Headache and seizures are two of the most frequent extracutaneous symptoms and they are caused by the growth of the lesion towar...

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Bibliographic Details
Published inArchivos argentinos de pediatría Vol. 120; no. 2; p. e75
Main Authors Vázquez Sánchez, María, Fuentelsaz Del Barrio, M Victoria, Conejero Del Mazo, Raquel, Genzor Ríos, Cristina, López Campos, Mónica, Valer Martínez, Ana
Format Journal Article
LanguageSpanish
Published Argentina 01.04.2022
Subjects
Disease Progression
Female
Headache
Humans
Methotrexate
Scleroderma, Localized - complications
Scleroderma, Localized - diagnosis
Scleroderma, Localized - drug therapy
Skin
dermatology
localized scleroderma
pediatrics
morphea
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Summary:Linear morphea in coup de sabre is a dermatological entity characterized by progressive, sclerosing inflammation of the skin tissue in the frontal region and on the scalp. Headache and seizures are two of the most frequent extracutaneous symptoms and they are caused by the growth of the lesion towards underlying structures. An early diagnosis is important to stop cranial progression and try to avoid secondary complications, mainly neurological. The diagnosis is relied on Morfea lineal en golpe de sable: a propósito de un caso Linear morphea in saber coup: about a case compatible clinical signs and a pathological study that allows a definitive confirmation. The treatment of choice is combination therapy with oral corticosteroids and methotrexate. Despite an adequate pharmacological treatment, this pathology can present a recurrent course and cause long-term sequelae. We present the case of a girl who was diagnosed quickly, despite a not very noticeable symptoms. She has been treated with oral methotrexate with a good response, without side effects.
ISSN:1668-3501