Ventricular septal aneurysm in a patient with Marfan syndrome

This is the first description of a patient with Marfan syndrome and an aneurysm of the ventricular septum. Apart from a borderline dilatation of the ascending aorta, there were no cardiovascular manifestations of Marfan syndrome. A transesophageal echocardiographic examination showed a large aneurys...

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Bibliographic Details
Published inZeitschrift für Kardiologie Vol. 89; no. 8; p. 702
Main Authors Bauer, M, Siniawski, H, Bauer, U, Gülmez, H, Knollmann, F, Lange, P E, Hetzer, R
Format Journal Article
LanguageGerman
Published Germany 01.08.2000
Subjects
Adult
Angiography
Echocardiography, Transesophageal
Female
Heart Aneurysm - diagnosis
Heart Aneurysm - diagnostic imaging
Heart Aneurysm - surgery
Heart Septal Defects, Ventricular - complications
Heart Septal Defects, Ventricular - diagnosis
Heart Septum
Heart Ventricles
Humans
Marfan Syndrome - complications
Tomography, X-Ray Computed
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Summary:This is the first description of a patient with Marfan syndrome and an aneurysm of the ventricular septum. Apart from a borderline dilatation of the ascending aorta, there were no cardiovascular manifestations of Marfan syndrome. A transesophageal echocardiographic examination showed a large aneurysm of the ventricular septum. To prevent the imminent rupture and the acute occurrence of a significant left-to-right-shunt on the ventricular level, as well as increasing irritation of tricuspid valve, an elective operation was performed. Besides the routine cardiological diagnostics, the search for intracardial defects is also necessary in patients with Marfan syndrome.
ISSN:0300-5860