Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis

IntroductionUnilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations. CaseA 29-year-old female at third trimester of twin pr...

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Published inRespiratory medicine case reports Vol. 43; p. 101834
Main Authors Wong, Yen Shen, Abidin, Zakhirati Zainol, Musa, Aisya Natasya, Kadir, Roqiah Fatmawati Abdul, Johari, Bushra
Format Report
LanguageEnglish
Published 01.01.2023
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Summary:IntroductionUnilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations. CaseA 29-year-old female at third trimester of twin pregnancy presented with massive hemoptysis. Computed tomography angiogram (CTA) showed unilateral absence of the right pulmonary artery with multiple dilated tortuous bronchial arteries supplying the right lung. Selective embolization of the bronchial artery was performed post-partum. ConclusionClinicians should have a high clinical suspicion of collateral artery bleeding in patients who present with unexplained hemoptysis and typical UPAA radiographic findings.
Bibliography:ObjectType-Case Study-2
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SourceType-Reports-1
ObjectType-Report-1
ISSN:2213-0071
2213-0071
DOI:10.1016/j.rmcr.2023.101834