Successful liver transplantation for non-resectable desmoplastic nested spindle cell tumor complicated by Cushing's syndrome

Desmoplastic spindle cell tumors of liver are rare tumors of low malignant potential characterized by well-demarcated nests of spindle and epithelioid cells in a dense desmoplastic stroma. While surgery remains the definitive treatment, there have been reports of tumor recurrence locally and metasta...

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Bibliographic Details
Published inPediatric transplantation Vol. 21; no. 6
Main Authors Tehseen, Sarah, Rapkin, Louis, Schemankewitz, Erwin, Magliocca, Joseph F, Romero, Rene
Format Report
LanguageEnglish
Published 01.09.2017
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Summary:Desmoplastic spindle cell tumors of liver are rare tumors of low malignant potential characterized by well-demarcated nests of spindle and epithelioid cells in a dense desmoplastic stroma. While surgery remains the definitive treatment, there have been reports of tumor recurrence locally and metastasis which respond poorly to chemotherapy. Hepatic transplant has been attempted in cases of recurrence or large size of primary tumor. Long-term follow-up and imaging surveillance are required as these tumors have shown a tendency for recurrence many years after initial therapy.
Bibliography:ObjectType-Case Study-2
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ObjectType-Report-1
ISSN:1399-3046
DOI:10.1111/petr.13000