Anesthetic Management of a Patient with Kennedy's Disease

Kennedy's disease, a rare x-linked disorder, has unique perioperative anesthetic considerations due to progressive spinal and lower motor degeneration. Bulbar involvement can lead to spontaneous laryngospasm, aspiration, and inadequate ventilation requiring postoperative respiratory support.1 S...

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Bibliographic Details
Published inThe international student journal of nurse anesthesia Vol. 21; no. 2; pp. 11 - 15
Main Author Gregorczyk, Magdalena
Format Journal Article
LanguageEnglish
Published Saint Louis International Student Journal of Nurse Anesthesia 01.07.2022
Subjects
Airway management
Androgens
Atrophy
Case reports
Chronic pain
Dysphagia
Endoscopy
Esophagus
Fentanyl
Gastrointestinal surgery
General anesthesia
Hyperlipidemia
Intubation
Liver diseases
Metabolism
Patients
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Summary:Kennedy's disease, a rare x-linked disorder, has unique perioperative anesthetic considerations due to progressive spinal and lower motor degeneration. Bulbar involvement can lead to spontaneous laryngospasm, aspiration, and inadequate ventilation requiring postoperative respiratory support.1 Spinal motor involvement causing muscle wasting requires careful titration of nondepolarizing neuromuscular blockers and avoidance of depolarizing neuromuscular blockers.1 Although Kennedy's disease is uncommon, a combination of a high frequency of misdiagnoses and a slowly progressing disease course makes these individuals likely candidates for requiring anesthetic care.2 Currently, case studies in the literature are limited, with few recommendations regarding anesthetic care.
ISSN:2688-5263