C44 IMMUNODEFICIENCY: CASE REPORTS: Granulomatous-Lymphocytic Interstitial Lung Disease In Common Variable Immunodeficiency: A Case Report

Introduction: Pulmonary manifestations in Common Variable Immunodeficiency (CVID), the most common primary immunodeficiency, are common and include acute infections, airways disease (bronchitis, bronchiectasis, bronchiolitis), and interstitial lung disease (ILD). Laboratory analyses showed: microcyt...

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Published inAmerican journal of respiratory and critical care medicine Vol. 195
Main Authors Kwon, M, Zaied, A, Mira-Avendano, I, Khoor, A, Leventhal, J
Format Journal Article
LanguageEnglish
Published New York American Thoracic Society 01.01.2017
Subjects
Biopsy
Bronchitis
Lung diseases
Lymphatic system
Pneumonia
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Summary:Introduction: Pulmonary manifestations in Common Variable Immunodeficiency (CVID), the most common primary immunodeficiency, are common and include acute infections, airways disease (bronchitis, bronchiectasis, bronchiolitis), and interstitial lung disease (ILD). Laboratory analyses showed: microcytic anemia, thrombocytopenia, low IgA level with normal IgG and IgM levels (she received IVIG just prior to presentation), normal alpha-1 antitrypsin levels, and negative serologies for autoimmune diseases (ANA, dsDNA, Scl 70, RNP, SS-A, SS-B, Jo 1, Sm, RF, CCP, c-ANCA, p-ANCA, C3, C4), myeloproliferative diseases, tuberculosis, fungus, and HIV.
ISSN:1073-449X
1535-4970