Experience of endotracheal intubation using video styletscope in a patient with mucopolysaccharidoses -A case report

• Published in: Anesthesia and pain medicine (Korean society of anesthesiologists) pp. 64 - 67
• Main Authors: 주효성, 김명희, 이애령, 박희경
• Format: Journal Article
• Language: English
• Published: 대한마취통증의학회 01.01.2013
• Subjects: 마취과학
• ISSN: 1975-5171; 2383-7977

Mucopolysaccharidoses (MPSs) are a group of inherited heterogenous metabolic disorders, caused by deficiency of an enzyme involved in the degradation of mucopolysaccharides, and thus deposition of mucopolysaccharides in all connective tissue. MPS type III is heparan sulphate storage disorder, especially marked central nervous system involvement. As with all the MPS disorders,this patient with MPS III presents coarse outlook features, such as macrocephaly, macroglossia, prominent mandible, short neck, and unstable atlantoaxial joints, as well as tracheal abnormality. These clinical findings give significant challenges to the anesthesiologist for adequate airway management and tracheal intubation. Recently,a number of new devices have been developed to facilitate intubation. We report an experience of facilitated tracheal intubation using video styletscope (OptiScope PM201Ⓡ, Pacific Medical, Seoul,Korea) in a 16 year old male patient with MPS III, who was undergoing inguinal hernia repair. KCI Citation Count: 0