회장 말단부에 궤양을 동반한 혈구탐식증후군 1예

• Published in: The Korean journal of gastroenterology pp. 205 - 209
• Main Authors: 문재현, 홍성표, 박필원, 고광현, 황성규, 임규성, 안희정, 강명서
• Format: Journal Article
• Language: Korean
• Published: 대한소화기학회 01.09.2006
• Subjects: 내과학
• ISSN: 1598-9992; 2233-6869

Reactive hemophagocytic syndrome or hemophagocytic lymphohistiocytosis, is characterized by the proliferation of benign histiocytes showing phagocytosis of blood cells in hematopoietic organs including bone marrow, spleen, or lymph nodes, accompanied by fever, hepatosplenomegaly, hepatic dysfunction, pancytopenia, and hypertriglyceridemia. The pathogenesis of reactive hemophagocytic syndrome is unknown. It is often associated with infection, malignant neoplasm, autoimmune disease, drugs and various immunodeficiencies. The prognosis of this syndrome is poor and the causes of death are hemorrhage, infection, or multiorgan failure. We experienced a case of hemophagocytic syndrome with terminal ileal ulcers, not associated with other causes. Thus, we report this case with a review of literatures. KCI Citation Count: 0