Solitary mastocytoma presenting at birth

Mastocytosis is a rare disease which occurs in both children and adults, and it can manifest as a solitary or multiple skin lesions. Both can cause cutaneous or systemic symptoms. Because of the heterogeneity of clinical presentation of mastocytosis and its rare prevalence, it can be hard to suspect...

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Bibliographic Details
Published inArchives of craniofacial surgery Vol. 19; no. 2; pp. 127 - 130
Main Authors Ha, Non Hyeon, Lee, Yoo Jung, Park, Myong Chul, Lee, Il Jae, Kim, Sue Min, Park, Dong Ha
Format Journal Article
LanguageKorean
Published 2018
Subjects
Mastocytoma
Mast cells
Cutaneous mastocytosis
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Summary:Mastocytosis is a rare disease which occurs in both children and adults, and it can manifest as a solitary or multiple skin lesions. Both can cause cutaneous or systemic symptoms. Because of the heterogeneity of clinical presentation of mastocytosis and its rare prevalence, it can be hard to suspect the mastocytosis at the first time. Most solitary mastocytomas are about 1-5 cm in diameter and have features of brownish-yellow, minimally elevated plaques with a smooth shiny surface. This article presents a case of solitary mastocytoma which occurred in neonate and that we treated through surgical excision. In histopathological examination, it consisted of c-kit-positive mast cells. Although pediatric cutaneous mastocytosis might regress spontaneously, clinicians should keep in mind that it could be associated with systemic mastocytosis which involves hematopoietic system.
Bibliography:KISTI1.1003/JNL.JAKO201819355173089
ISSN:2287-1152
2287-5603