Perivascular epithelioid cell tumor (PEComa) of the ascending colon: the implication of IFN-${\alpha}$ 2b treatment

A 7-year-old boy presented with hematochezia and abdominal pain. A 3.7-cm-sized mass was identified in the ascending colon by abdominal computed tomography and colonoscopy. The patient underwent surgical resection. Pathological examination revealed a low-grade perivascular epithelioid cell tumor (PE...

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Bibliographic Details
Published inKorean journal of pediatrics Vol. 53; no. 11; pp. 975 - 978
Main Authors Park, Sun-Ju, Han, Dong-Kyun, Baek, Hee-Jo, Chung, Sang-Young, Nam, Jong-Hee, Kook, Hoon, Hwang, Tai-Ju
Format Journal Article
LanguageKorean
Published 2010
Subjects
PEComa
Interferon-alpha
Perivascular epithelioid cell tumor
Colon
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Summary:A 7-year-old boy presented with hematochezia and abdominal pain. A 3.7-cm-sized mass was identified in the ascending colon by abdominal computed tomography and colonoscopy. The patient underwent surgical resection. Pathological examination revealed a low-grade perivascular epithelioid cell tumor (PEComa). PEComa in the colon is very rare. Only a few cases have been reported so far. An effective treatment method for this rare tumor has not been established yet. The patient received adjuvant interferon-${\alpha}$ immunotherapy for 1 year. He has been tumor-free for 26 months since the initial diagnosis. This report is the first documented case of the use of interferon-${\alpha}$ for pediatric PEComa of the colon.
Bibliography:KISTI1.1003/JNL.JAKO201018651618600
ISSN:1738-1061
2092-7258