이달의 X-선 : 다기관 침범을 동반한 거대 폐 모세포종

• Published in: Tuberculosis and respiratory diseases Vol. 62; no. 2; pp. 149 - 153
• Main Authors: 이태환, Tae Hwan Lee, 이가영, Ka Young Lee, 김소리, So Ri Kim, 민경훈, Kyung Hun Min, 박성주, Seoung Ju Park, 이흥범, Heung Bum Lee, 이양근, Yang Keun Rhee, 이용철, Yong Chul Lee
• Format: Journal Article
• Language: Korean
• Published: 대한결핵 및 호흡기학회 28.02.2007
• Subjects: Lung cancer; Metastasis; Pulmonary blastoma
• ISSN: 1738-3536; 2005-6184

폐모세포종은 폐종양으로 매우 드물게 나타나며 드물게 간, 흉외 림프절, 심장으로 전이된다고 보고되고 있다. 본 저자들은 복부의 팽만감과 통증 및 호흡곤란을 주소로 내원한 환자에서 간과 폐의 거대 종괴를 발견하였고, 조직 검사를 통하여 간, 횡격막, 심장 등 다발성 침범을 동반한 폐모세포종으로 진단받은 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다. A pulmonary blastoma is a rare malignant tumor of the lung that is composed of epithelial and mesenchymal elements and resembles the structure of an embryonic lung. Pulmonary blastomas have a very poor prognosis and make up 0.25 to 0.5 percent of all primary malignant lung tumors. A pulmonary blastoma usually manifests as a solitary parenchymal mass or nodule and multiple subpleural mass with effusion on chest X-ray and computed tomography. We encountered a very rare case of pulmonary blastoma in a 52 years old male. He complained of abdominal pain, fullness, and dyspnea. The radiology examination revealed a huge lung mass invading the mediastinum, heart, diaphragm, and liver. The percutaneous needle biopsies were performed, and this tumor was diagnosed as a pulmonary blastoma. We report a biopsy confirmed case of a huge pulmonary blastoma invading multiple organs. (Tuberc Respir Dis 2007; 62: 149-153)