Formula powder for urea cycle disorder and preparation method thereof

• Main Authors: ZHANG SIJIE, ZENG ZHEN, SUN HONGFENG
• Format: Patent
• Language: Chinese; English
• Published: 06.03.2018
• Subjects: FOODS OR FOODSTUFFS; FOODS, FOODSTUFFS, OR NON-ALCOHOLIC BEVERAGES, NOT COVERED BYSUBCLASSES A23B - A23J; HUMAN NECESSITIES; INDEXING SCHEME RELATING TO FOODS, FOODSTUFFS OR NON-ALCOHOLICBEVERAGES; PRESERVATION OF FOODS OR FOODSTUFFS, IN GENERAL; THEIR PREPARATION OR TREATMENT, e.g. COOKING, MODIFICATION OFNUTRITIVE QUALITIES, PHYSICAL TREATMENT; THEIR TREATMENT, NOT COVERED BY OTHER CLASSES

The invention relates to formula powder for a urea cycle disorder and a preparation method thereof. The formula powder is prepared from vegetable oil fat powder, amino acid, fatty acid, algal oil, compound vitamin and compound mineral substances through a dry method. By the adoption of the amino acid and elimination of unnecessary amino acids (alanine, arginine, aspartic acid, asparaginate, glutamic acid, glutamine, glycine, proline and serine), on one hand, the formula powder for the urea cycle disorder can guarantee nutrition supplementation of a patient, and on the other hand, the blood ammonia concentration of the patient can be effectively controlled to relieve a burden on the liver and guarantee normal metabolism of the body of the patient. The formula is scientific in proportion ofnutritional components, and is extremely high in dissolubility and stability. The preparation method is simple, easy to operate and suitable for large-scale industrial production. 本发明涉及种用于尿素循环障碍的配方粉及其制备方法，所述配方粉由植物油脂肪粉、氨基酸、脂肪酸