Powdered formula for tyrosinemia and preparation method thereof

• Main Authors: ZHANG SIJIE, ZENG ZHEN, SUN HONGFENG
• Format: Patent
• Language: Chinese; English
• Published: 09.01.2018
• Subjects: FOODS OR FOODSTUFFS; FOODS, FOODSTUFFS, OR NON-ALCOHOLIC BEVERAGES, NOT COVERED BYSUBCLASSES A23B - A23J; HUMAN NECESSITIES; PRESERVATION OF FOODS OR FOODSTUFFS, IN GENERAL; THEIR PREPARATION OR TREATMENT, e.g. COOKING, MODIFICATION OFNUTRITIVE QUALITIES, PHYSICAL TREATMENT; THEIR TREATMENT, NOT COVERED BY OTHER CLASSES

The invention relates to a powdered formula for tyrosinemia and a preparation method thereof. The powdered formula is composed of vegetable fat powder, amino acids, fatty acids, algal oil, compound vitamins and compound mineral substances, and is prepared by a dry preparation process. According to the powdered formula disclosed by the invention, the amino acids are adopted, and phenylalanine and tyrosine are removed, so on the one hand, nutritional supplement of a patient can be ensured; on the other hand, the content of the phenylalanine and tyrosine in the body of the patient can be effectively controlled. The formula is scientific in ratio and nutritional and has excellent solubility and stability. The preparation method is simple and easy to operate and is suitable for large-scale industrial production. 本发明涉及种用于酪氨酸血症的配方粉及其制备方法，所述配方粉由植物油脂肪粉、氨基酸、脂肪酸、藻油、复合维生素、复合矿物质组成，通过干法制备工艺制得；所述配方粉采用氨基酸并去除苯丙氨酸和酪氨酸，方面可保证患者的营养补充，另方面可有效控制患者体内的苯丙氨酸和酪氨酸含量。该配方科学配比营养组件，溶解性及稳定性很好。制备方法简单易操作，适合规模化工业生产。