Persistent truncus arteriosus with double aortic arch and mitral stenosis

• Published in: Pediatric cardiology Vol. 34; no. 8; pp. 2024 - 2026
• Main Authors: Imai, Kenta, Tsukuda, Kazuya, Sakazaki, Hisanori, Fujiwara, Keiichi
• Format: Journal Article
• Language: English
• Published: United States 2013
• Subjects: Abnormalities, Multiple; Aorta, Thoracic - abnormalities; Blalock-Taussig Procedure - methods; Echocardiography; Female; Follow-Up Studies; Humans; Infant, Newborn; Mitral Valve Stenosis - congenital; Mitral Valve Stenosis - diagnosis; Mitral Valve Stenosis - surgery; Multidetector Computed Tomography; Truncus Arteriosus, Persistent - diagnosis; Truncus Arteriosus, Persistent - surgery; Vascular Malformations - diagnosis; Vascular Malformations - surgery
• ISSN: 1432-1971
• DOI: 10.1007/s00246-012-0572-5

This report describes a case involving the rare combination of persistent truncus arteriosus type A2, double aortic arch, and mitral stenosis. At the age of 26 days, the patient underwent division of the right-sided aortic arch with tracheal compression and bilateral pulmonary banding. Fontan completion was successfully achieved after separation of the pulmonary artery from the arterial trunk, atrial septostomy, and modified Blalock-Taussig shunt at the age of 7 months and bilateral bidirectional Glenn anastomosis at the age of 1 year and 3 months. At this writing, the patient is doing well 2 years and 6 months after Fontan completion.