Pentalogy of Cantrell. A case report

Ectopia cordis is an extremely rare cardiac anomaly. The heart is localized partially or totally outside the thorax cavity. This anomaly occurs as an isolated defect or combined with others midline defects. Cantrell and colleagues described, in 1958, a syndrome including defects of the abdominal wal...

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Published inArchivos de cardiología de México Vol. 76; no. 2; pp. 202 - 207
Main Authors Hernández-González, Martha, Jiménez-Arteaga, Santiago, Ortega, Francisco, Solorio, Sergio, Martínez-Flores, Enrique, David-Gómez, Felipe, Sánchez-Soberanis, Agustín, Ortegón-Cerdeña, José, López-Gallegos, Diana, Argüero-Sánchez, Rubén, Alva, Carlos
Format Journal Article
LanguageSpanish
Published Mexico 01.04.2006
Subjects
Abdominal Wall - abnormalities
Abnormalities, Multiple - diagnosis
Abnormalities, Multiple - surgery
Child
Diaphragm - abnormalities
Heart Defects, Congenital - diagnosis
Heart Defects, Congenital - surgery
Humans
Male
Pericardium - abnormalities
Sternum - abnormalities
Syndrome
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Summary:Ectopia cordis is an extremely rare cardiac anomaly. The heart is localized partially or totally outside the thorax cavity. This anomaly occurs as an isolated defect or combined with others midline defects. Cantrell and colleagues described, in 1958, a syndrome including defects of the abdominal wall, sternum, diaphragm, pericardium and heart. There are few successful surgical cases with this pentalogy. We describe a case with this Cantrell's pentalogy. The cardiac malformation was a univentricular heart with pulmonary stenosis. The patient underwent successful surgical palliation with a systemic-to-pulmonary anastomosis and uneventful recovering.
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ISSN:1405-9940