Diagnostic criteria of atypical benign partial epilepsy syndrome in childhood

• Published in: Zhurnal nevrologii i psikhiatrii imeni S.S. Korsakova Vol. 101; no. 1; p. 13
• Main Authors: Mukhin, K Iu, Glukhova, L Iu, Petrukhin, A S, Iukhalina, N S, Gaman, O V
• Format: Journal Article
• Language: Russian
• Published: Russia (Federation) 2001
• Subjects: Anticonvulsants - therapeutic use; Aphasia - diagnosis; Aphasia - etiology; Brain - pathology; Child; Child, Preschool; Electroencephalography; Epilepsies, Partial - complications; Epilepsies, Partial - diagnosis; Epilepsies, Partial - drug therapy; Epilepsy, Absence - complications; Epilepsy, Absence - diagnosis; Epilepsy, Absence - drug therapy; Epilepsy, Rolandic - complications; Epilepsy, Rolandic - diagnosis; Epilepsy, Rolandic - drug therapy; Female; Humans; Magnetic Resonance Imaging; Male; Neuropsychological Tests; Severity of Illness Index; Treatment Outcome
• ISSN: 1997-7298

The paper presents an analysis of clinical-neuropsychological peculiarities of the syndrome of atypical benign partial childhood epilepsy (pseudolennox syndrome) of 6 patients (3 boys, 3 girls). An age of the onset of the disease was between 1.5-4 years. There was polymorphism of paroxysms, their high frequency with an obligate presence of hemifacial fits and atypical absences. Night generalized tonic-clonic attacks and the falling attacks were found in 67% of the patients. Spectrum of the neurological disorders included disorders of speech and a slight cerebella symptomatology. Regional "rolandic" activity and diffuse epileptiformed disorders, increasing into a phase of a slow sleep, were registered by EEG. Resistance to anticonvulsive therapy was revealed. The authors had demonstrated a nosologic independence of pseudolennox syndrome and had considered worth while to pick it out in a group of cryptogenic partial forms of epilepsy together with the epileptic aphasia of Landu-Kleffner and an epilepsy with the continuous peak-waves during the slow sleep.