Malignant cutaneous lymphoma in a case of Wiskott-Aldrich syndrome with long-term survival

The case of a 24 year old man affected with Wiskott-Aldrich syndrome (WAS) is reported. The review of the charts of previous hospital admissions revealed the presence of an inherited trait and a long history of recurrent infections and hemorrhages. This young man was referred to our surgical departm...

Full description

Saved in:
Bibliographic Details
Published inMinerva medica Vol. 81; no. 5; p. 427
Main Authors Ghilardi, G, Pecis, C, Bortolani, E M, De Bitonto, A
Format Journal Article
LanguageItalian
Published Italy 01.05.1990
Subjects
Adult
Biopsy
Gangrene
Humans
Leg
Lymphoma - etiology
Lymphoma - pathology
Male
Skin Neoplasms - etiology
Skin Neoplasms - pathology
Wiskott-Aldrich Syndrome - complications
Wiskott-Aldrich Syndrome - pathology
Online AccessGet more information

Cover

More Information
Summary:The case of a 24 year old man affected with Wiskott-Aldrich syndrome (WAS) is reported. The review of the charts of previous hospital admissions revealed the presence of an inherited trait and a long history of recurrent infections and hemorrhages. This young man was referred to our surgical department with the diagnosis of right lower limb gangrene, but the biopsy showed the lesion being due to cutaneous malignant lymphoma characterized by large polymorphic cells. All clinical and immunological elements typical of WAS were present: they are discussed with regard to the recent literature.
ISSN:0026-4806