A dermatopathic Juvenile Dermatomyositis; An Unexpected Case in Childhood

Juvenile dermatomyositis (JDM) is a rare idiopathic inflammatory disease, which usually presents with skin rashes along with muscle weakness. We report a case of JDM in a 10- year-old girl with no skin manifestations presenting with progressive muscle weakness and fatigue. Further laboratory investi...

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Published inIranian journal of child neurology Vol. 14; no. 3; pp. 89 - 92
Main Authors Yeganeh, Mehrnoush Hassas, Ahmadi, Pooria, Nilipour, Yalda, Khorshidi, Mohadese Sadat Mousavi, Sinaei, Reza, Fathi, Mohammad Reza, Shiari, Reza
Format Journal Article
LanguageEnglish
Published Tehran Iranian Child Neurology Society 01.06.2020
Shahid Beheshti University of Medical Sciences
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Summary:Juvenile dermatomyositis (JDM) is a rare idiopathic inflammatory disease, which usually presents with skin rashes along with muscle weakness. We report a case of JDM in a 10- year-old girl with no skin manifestations presenting with progressive muscle weakness and fatigue. Further laboratory investigations, along with a muscle biopsy, confirmed the diagnosis of adermatopathic JDM. The patient was treated with intravenous immunoglobulin, corticosteroids, methotrexate, hydroxychloroquine, pamidronate, and rituximab. Following treatment, patients' symptoms subsided, and she gained normal muscular strength over a year.
ISSN:1735-4668
2008-0700
DOI:10.22037/ijcn.v14i3.21686