Peutz-Jeghers syndrome: case report

A case of Peutz-Jeghers syndrome (PJS) in an African girl is presented to document the clinical presentation, management and follow up of this condition. The patient who presented with black buccal mucosal hyperpigmentation and clinical features of jejuno-jejunal intussusception was successfully man...

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Bibliographic Details
Published inEast African medical journal Vol. 76; no. 5; p. 284
Main Authors Igun, G O, Ameh, Y Y, Awani, K U
Format Journal Article
LanguageEnglish
Published Kenya 01.05.1999
Subjects
Abdominal Pain - etiology
Aftercare - methods
Child
Clinical Protocols
Female
Humans
Intestinal Polyps - etiology
Intestinal Polyps - surgery
Intussusception - etiology
Intussusception - surgery
Jejunal Diseases - etiology
Jejunal Diseases - surgery
Mass Screening
Nigeria
Peutz-Jeghers Syndrome - complications
Peutz-Jeghers Syndrome - diagnosis
Sigmoid Diseases - etiology
Sigmoid Diseases - surgery
Nigeria
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Summary:A case of Peutz-Jeghers syndrome (PJS) in an African girl is presented to document the clinical presentation, management and follow up of this condition. The patient who presented with black buccal mucosal hyperpigmentation and clinical features of jejuno-jejunal intussusception was successfully managed by operative reduction of the intussusception and polypectomy. She is being followed up for evidence of malignant transformation in associated intestinal polyps and development of extra-intestinal malignancies at other sites. The management of PJS in light of recent trends is discussed, especially with reference to suggested protocols for screening and surveillance of sites at supposed risk of tumour development.
ISSN:0012-835X