Fundus flavimaculatus with severely reduced cone electroretinogram

An 11-year-old girl complaining of progressive visual loss in both eyes showed atrophic macular degeneration with yellowish white flecks around the fovea in both eyegrounds. Decreased vision, central scotoma with normal peripheral visual field, and angiographic dark choroid except for transmitted hy...

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Bibliographic Details
Published inJapanese journal of ophthalmology Vol. 36; no. 3; p. 249
Main Authors Iijima, H, Gohdo, T, Hosaka, O
Format Journal Article
LanguageEnglish
Published Japan 1992
Subjects
Child
Dark Adaptation
Electroretinography
Female
Fluorescein Angiography
Fundus Oculi
Humans
Macular Degeneration - physiopathology
Photoreceptor Cells - physiopathology
Retinal Degeneration - physiopathology
Scotoma - diagnosis
Visual Fields
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Summary:An 11-year-old girl complaining of progressive visual loss in both eyes showed atrophic macular degeneration with yellowish white flecks around the fovea in both eyegrounds. Decreased vision, central scotoma with normal peripheral visual field, and angiographic dark choroid except for transmitted hyperfluorescence in the macula and at the flecks confirmed the diagnosis of fundus flavimaculatus with atrophic macula. Electroretinograms, however, revealed severely reduced cone responses associated with almost normal rod response, which led to the diagnosis of cone dystrophy. The rare combination of angiographic evidence of fundus flavimaculatus and electroretinographically diagnosed cone dystrophy was discussed.
ISSN:0021-5155