Fibromuscular dysplasia causing atypical coarctation of the thoracic aorta: histological presentation of a case

The authors report a case of atypical coarctation of the thoracic aorta discovered by chance in a 37-year-old man, victim of a car accident. The angiogram revealed a "string-of-beads" contour in the coarctate area while the left subclavian artery presented a severe stenosis at its origin....

Full description

Saved in:
Bibliographic Details
Published inVASA Vol. 24; no. 2; p. 194
Main Authors Vuong, P N, Janzen, J, Bical, O, Susa-Uva, M
Format Journal Article
LanguageEnglish
Published Switzerland 1995
Subjects
Adult
Aorta, Thoracic - pathology
Aortic Coarctation - pathology
Fibromuscular Dysplasia - pathology
Humans
Male
Muscle, Smooth, Vascular - pathology
Online AccessGet more information

Cover

More Information
Summary:The authors report a case of atypical coarctation of the thoracic aorta discovered by chance in a 37-year-old man, victim of a car accident. The angiogram revealed a "string-of-beads" contour in the coarctate area while the left subclavian artery presented a severe stenosis at its origin. Vascular checkup examination failed to identify any additional vascular anomaly. The patient underwent surgical resection, with a Dacron prosthetic bypass. Histological study of the specimen removed, showed a typical perimedial and extensive medial types of fibromuscular dysplasia (FMD) of the aorta. Pathogenesis of this disease is discussed.
ISSN:0301-1526