Fibular dimelia with deficiency of the tibia

Longitudinal deficiency of the tibia associated with fibular dimelia is a very rare condition. We report our experience with six patients and outline management of this anomaly. Knee disarticulation is advised in cases with an associated normal femur, and femorofibular fusion is advised in cases of...

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Bibliographic Details
Published inJournal of pediatric orthopaedics Vol. 13; no. 2; p. 203
Main Authors Kumar, A, Kruger, L M
Format Journal Article
LanguageEnglish
Published United States 01.03.1993
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Summary:Longitudinal deficiency of the tibia associated with fibular dimelia is a very rare condition. We report our experience with six patients and outline management of this anomaly. Knee disarticulation is advised in cases with an associated normal femur, and femorofibular fusion is advised in cases of associated ipsilateral proximal focal femoral deficiency (PFFD) or congenital short femur. Fibulocalcaneal fusion and Boyd type amputation provide good end-bearing stumps.
ISSN:0271-6798
1539-2570