A rare case of suspected lupus erythematous panniculitis as the presenting skin feature of juvenile dermatomyositis: A case report

Juvenile dermatomyositis is a rare autoimmune myopathy of childhood, associated with systemic vasculopathy, primarily affecting the capillaries. Panniculitis is seen histologically in about 10% of patients with dermatomyositis; however, its clinical presentation is rare, with only 30 cases presented...

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Published inSAGE open medical case reports Vol. 10; p. 2050313X221086317
Main Authors Ginter, Dylan C, Ramien, Michele L, Brundler, Marie-Anne, Swaney, Laura C, Miettunen, Paivi Mh, Luca, Nadia Jc
Format Journal Article
LanguageEnglish
Published England SAGE Publications 01.03.2022
Subjects
JCMS Case Report
Juvenile dermatomyositis
panniculitis
lupus erythematosus panniculitis
inflammatory bowel disease
lupus panniculitis
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Summary:Juvenile dermatomyositis is a rare autoimmune myopathy of childhood, associated with systemic vasculopathy, primarily affecting the capillaries. Panniculitis is seen histologically in about 10% of patients with dermatomyositis; however, its clinical presentation is rare, with only 30 cases presented in the literature to date. The histopathology overlaps with other inflammatory disease states, and is almost identical to the panniculitis seen in lupus erythematous panniculitis. In the cases with both panniculitis and dermatomyositis, skin and muscle inflammation is usually the first clinical manifestation. We present a case of a 16-year-old female with panniculitis as the initial presenting feature of juvenile dermatomyositis in the context of a prior diagnosis of indeterminate colitis.
ISSN:2050-313X
2050-313X
DOI:10.1177/2050313X221086317