Epidemiological evaluation regarding the role of cystic fibrosis as a risk factor for child malnutrition

Cystic fibrosis (CF) is the most common monogenic autosomal recessive disorder with progressive chronic evolution which is potentially lethal. Poor growth is a characteristic of children suffering from cystic fibrosis. A poor nutritional status is an independent risk factor for inadequate survival i...

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Published inRevista medico-chirurgicala a Societatii de Medici si Naturalisti din Iasi Vol. 118; no. 2; p. 450
Main Authors Florescu, Laura, Paduraru, Dana Teodora Anton, Mîndru, Dana Elena, Temneanu, Oana Raluea, Petrariu, F D, Matei, Mioara Calipsoana
Format Journal Article
LanguageEnglish
Published Romania 01.04.2014
Subjects
Body Weight
Child
Cystic Fibrosis - complications
Cystic Fibrosis - diagnosis
Cystic Fibrosis - epidemiology
Cystic Fibrosis - therapy
Disease Progression
Energy Intake
Humans
Life Expectancy
Malnutrition - diagnosis
Malnutrition - epidemiology
Malnutrition - etiology
Malnutrition - therapy
Nutritional Requirements
Nutritional Status
Quality of Life
Risk Factors
Romania - epidemiology
Romania
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Summary:Cystic fibrosis (CF) is the most common monogenic autosomal recessive disorder with progressive chronic evolution which is potentially lethal. Poor growth is a characteristic of children suffering from cystic fibrosis. A poor nutritional status is an independent risk factor for inadequate survival in cystic fibrosis and is associated with disease complications. The appropriate nutritional management is an important part of the treatment so that the patient with cystic fibrosis can achieve normal growth and development and maintain the best possible health status. A balanced diet supplemented with snacks high in fat and calories is necessary to increase the caloric intake in children with cystic fibrosis. Children with cystic fibrosis have higher caloric needs than healthy children of the same age and sex. Malnutrition in CF is multifactorial. Cystic fibrosis is a complex multisystem disorder affecting mainly the gastrointestinal tract and respiratory system. In the past, malnutrition was an inevitable consequence of disease progression, leading to poor growth, impaired respiratory muscle function, decreased exercise tolerance and immunological impairment. A positive association between body weight and height and survival has been widely reported. The energy requirements of patients with CF vary widely and generally increase with age and disease severity. Cystic fibrosis remains a paediatric disorder which is often underdiagnosed but which, if therapeutically managed properly (by means of drug therapy as well as by appropriate physiotherapy techniques), can lead to improved quality of life and, thus, to a bigger life expectancy.
ISSN:0048-7848