A giant cranial aneurysmal bone cyst associated with fibrous dysplasia

An aneurysmal bone cyst (ABC) is a rare, benign fibro-osseous lesion, considered a vascular phenomenon secondary to fibrous dysplasia or a giant-cell tumour, and occurs mainly in long bones and vertebrae. In this case report a 16-year-old male presented with massive epistaxis. He was admitted with a...

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Bibliographic Details
Published inB-ENT (Leuven) Vol. 4; no. 1; p. 29
Main Authors Składzieriń, J, Olés, K, Zagólski, O, Moskała, M, Sztuka, M, Strek, P, Wierzchowski, W, Tomik, J
Format Journal Article
LanguageEnglish
Published Belgium 01.01.2008
Subjects
Adolescent
Bone Cysts, Aneurysmal - diagnosis
Bone Cysts, Aneurysmal - etiology
Bone Cysts, Aneurysmal - surgery
Chronic Disease
Epistaxis - etiology
Fibrous Dysplasia of Bone - complications
Headache - etiology
Humans
Male
Paranasal Sinuses - diagnostic imaging
Recurrence
Rhinitis - etiology
Tomography, X-Ray Computed
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Summary:An aneurysmal bone cyst (ABC) is a rare, benign fibro-osseous lesion, considered a vascular phenomenon secondary to fibrous dysplasia or a giant-cell tumour, and occurs mainly in long bones and vertebrae. In this case report a 16-year-old male presented with massive epistaxis. He was admitted with a 3-year history of chronic rhinitis, headaches, right ocular pain and recurrent epistaxis. CT scans showed a predominantly cystic, expansive mass obstructing both nasal cavities, extending to all paranasal sinuses and both orbits, with evidence of anterior cranial fossa skull base destruction. The patient underwent a craniofacial resection of the tumour performed with an external approach and an immediate reconstruction of the dural defect. Histology confirmed the lesion was an ABC associated with fibrous dysplasia. The patient's recovery was complete. A large facial aneurysmal bone cyst can damage the facial skeleton and skull base, and requires excision by a combined external approach.
ISSN:1781-782X