Echocardiographic features of non-compaction cardiomyopathy: missed and misdiagnosed disease

Non-compaction cardiomyopathy is a rare disease, anatomically characterized by a prominent trabecular pattern and deep intertrabecular recesses. Its clinical manifestations include severe left ventricular dysfunction, arrhythmias, systemic embolism, and sudden death. In this report, two cases of pat...

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Published inArquivos brasileiros de cardiologia Vol. 93; no. 2; pp. e33 - e35
Main Authors Martínez-Baca López, Francisco, Alonso Bravo, Rosa Marisol, Rodríguez Huerta, Domingo Arturo
Format Journal Article
LanguageEnglish
Published Brazil 01.08.2009
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Summary:Non-compaction cardiomyopathy is a rare disease, anatomically characterized by a prominent trabecular pattern and deep intertrabecular recesses. Its clinical manifestations include severe left ventricular dysfunction, arrhythmias, systemic embolism, and sudden death. In this report, two cases of patients of different ages with non-compaction cardiomyopathy are described: a male schoolboy whose pathology was associated with mitral stenosis and regurgitation and a 50-year-old female with history of high blood pressure and cardiac failure.
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ISSN:1678-4170
DOI:10.1590/S0066-782X2009000800024