Diffuse thoracic lymphangiomatosis: diagnosis and treatment

Histologically, lymphangiomatosis is a rare type of benign neoplasm caused by abnormal development and proliferation of the lymphatic system. Thoracic lymphangiomatosis can present in a localized (lymphangioma) or diffuse form (lymphangiomatosis). In most cases the disease progresses to serious morb...

Full description

Saved in:
Bibliographic Details
Published inArchivos de bronconeumología Vol. 40; no. 12; pp. 599 - 601
Main Authors Bermejo Casero, E J, Mongil Poce, R, Arrabal Sánchez, R, Fernández de Rota Avecilla, A, Benítez Doménech, A, Fernández Bermúdez, J L
Format Journal Article
LanguageSpanish
Published Spain 01.12.2004
Subjects
Adolescent
Adult
Female
Humans
Lymphangioleiomyomatosis - pathology
Lymphangioleiomyomatosis - radiotherapy
Male
Thoracic Neoplasms - pathology
Thoracic Neoplasms - radiotherapy
Online AccessGet full text

Cover

More Information
Summary:Histologically, lymphangiomatosis is a rare type of benign neoplasm caused by abnormal development and proliferation of the lymphatic system. Thoracic lymphangiomatosis can present in a localized (lymphangioma) or diffuse form (lymphangiomatosis). In most cases the disease progresses to serious morbidity or even death. The treatment of choice for localized disease is usually surgery or, less frequently, local injection of sclerosing agents (streptococcus antigen OK-432). However, in diffuse forms there is a gelatinous infiltrate without defined limits. In these cases the main treatment option is radiotherapy. We report 2 cases of diffuse thoracic lymphangiomatosis with pulmonary infiltrate. In both cases radiotherapy in appropriate doses successfully eliminated pulmonary infiltrates, pleural effusion, dyspnea, and general discomfort. Surgery was needed to resolve complications of the disease and for diagnosis.
Bibliography:ObjectType-Article-2
SourceType-Scholarly Journals-1
ObjectType-Feature-1
content type line 23
ObjectType-Report-3
ObjectType-Case Study-4
ISSN:0300-2896