Posterior polymorphous dystrophy, case report and literature review

• Published in: Archivos de la Sociedad Española de Oftalmología Vol. 90; no. 9; pp. 439 - 441
• Main Authors: Mendoza-Adam, G, Hernandez-Camarena, J C, Valdez-García, J E
• Format: Journal Article
• Language: Spanish
• Published: Spain 01.09.2015
• Subjects: Corneal Dystrophies, Hereditary - complications; Corneal Dystrophies, Hereditary - diagnosis; Corneal Dystrophies, Hereditary - epidemiology; Corneal Dystrophies, Hereditary - genetics; Corneal Dystrophies, Hereditary - pathology; Descemet Membrane - pathology; Diagnosis, Differential; Endothelium, Corneal - pathology; Female; Fuchs' Endothelial Dystrophy - diagnosis; Genes, Dominant; Humans; Mexico - epidemiology; Microscopy - methods; Middle Aged; Photophobia - etiology; Vision Disorders - etiology; Endotelio corneal; Distrofia corneal; Latinoamericano; Latinamerican; Corneal dystrophy; Corneal endothelium
• ISSN: 1989-7286
• DOI: 10.1016/j.oftal.2015.01.003

Posterior Polymorphous Dystrophy (DPP) is a rare posterior corneal dystrophy that is genetically transmitted as autosomal dominant. Corneal structures affected in this dystrophy are Descemet membrane and the endothelium. A case is presented on a 47 years old woman with no relevant history, with typical findings of DPP (vesicular and band lesions at the endothelium and posterior Descemet). To our knowledge there are no reported cases of DPP in Latin-American patients in the literature. The clinical manifestations in our patient were found to be very similar to the cases reported in other populations.