Dopamine-secreting pheochromocytoma with neurofibromatosis type 1 : a case report

Pheochromocytoma occurs in 0.1-5.7% of patients with neurofibromatosis type 1 (NF1), while dopamine-secreting pheochromocytoma is rare. We report here a rare case of dopamine-secreting pheochromocytoma in a patient with NF1. A 46-year-old woman with NF1 was referred to our hospital with epigastralgi...

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Published inHinyokika kiyo. Acta urologica Japonica Vol. 58; no. 10; pp. 543 - 547
Main Authors Nakazawa, Shigeaki, Kishikawa, Hidefumi, Akiyama, Kotaro, Yamanaka, Kazuaki, Hirai, Toshiaki, Nishimura, Kenji, Ichikawa, Yasuji
Format Journal Article
LanguageJapanese
Published Japan 01.10.2012
Subjects
Adrenal Gland Neoplasms - complications
Adrenal Gland Neoplasms - secretion
Adrenal Gland Neoplasms - surgery
Dopamine - secretion
Epinephrine - blood
Female
Humans
Middle Aged
Neurofibromatosis 1 - complications
Norepinephrine - blood
Pheochromocytoma - complications
Pheochromocytoma - secretion
Pheochromocytoma - surgery
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Summary:Pheochromocytoma occurs in 0.1-5.7% of patients with neurofibromatosis type 1 (NF1), while dopamine-secreting pheochromocytoma is rare. We report here a rare case of dopamine-secreting pheochromocytoma in a patient with NF1. A 46-year-old woman with NF1 was referred to our hospital with epigastralgia. The patient had no history of hypertension. Abdominal sonography incidentally revealed a left adrenal tumor, while abdominal computed tomography and magnetic resonance imaging findings showed a left adrenal tumor, sized 63×58 mm. Laboratory evaluations revealed exclusively elevated urine dopamine levels in addition to elevated serum adrenaline and noradrenaline levels. Laparoscopic left adrenalectomy was performed and the dopamine levels and other cathecolamine levels returned to normal postoperatively.
Bibliography:ObjectType-Case Study-2
SourceType-Scholarly Journals-1
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ISSN:0018-1994