Primary Cardiac Angiosarcoma with Superior Vena Cava Syndrome

Primary cardiac angiosarcoma is rare and its prognosis very poor. A 34-year-old woman complained of facial edema and dyspnea. Echocardiography, chest computed tomography scan and chest magnetic resonance imaging showed a huge tumor arising in the right atrium. Surgical excision of the tumor was perf...

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Bibliographic Details
Published inKyobu geka. The Japanese journal of thoracic surgery Vol. 69; no. 5; p. 370
Main Authors Shimada, Naohiro, Shiomi, Daisuke, Kaki, Nobuaki, Kiyama, Hiroshi
Format Journal Article
LanguageJapanese
Published Japan 01.05.2016
Subjects
Adult
Antibiotics, Antineoplastic - administration & dosage
Antineoplastic Agents, Alkylating - administration & dosage
Antineoplastic Combined Chemotherapy Protocols - therapeutic use
Doxorubicin - administration & dosage
Female
Heart Neoplasms - drug therapy
Heart Neoplasms - surgery
Hemangiosarcoma - drug therapy
Hemangiosarcoma - surgery
Humans
Ifosfamide - administration & dosage
Superior Vena Cava Syndrome - complications
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Summary:Primary cardiac angiosarcoma is rare and its prognosis very poor. A 34-year-old woman complained of facial edema and dyspnea. Echocardiography, chest computed tomography scan and chest magnetic resonance imaging showed a huge tumor arising in the right atrium. Surgical excision of the tumor was performed for the purpose of relieving superior vena cava syndrome and making diagnosis of the tumor. The right atrial wall, including the tumor, was resected and reconstructed with Gore Tex patch under cardiopulmonary bypass. The tumor was diagnosed as angiosarcoma. Doxorubicin hydrochloride/ifosfamide were used to treat postoperative cardiac recurrence and lung metastasis. These drugs were effective to a certain degree, but she died of brain metastasis of the tumor in the 14th postoperative month.
ISSN:0021-5252