Basal cell nevus syndrome and medulloblastoma: a case report

The basal cell nevus syndrome (BCNS) is a rare autosomal dominant disorder characterized by multiple nevoid basal-cell carcinomas of the skin, recurrent odontogenic keratocysts, skeletal anomalies, developmental malformations, and the predisposition to other neoplastic processes. Among the well know...

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Published inBoletin de la Asociación Médica de Puerto Rico Vol. 85; no. 1-3; p. 24
Main Authors Romero Pérez, J A, Lleras Santana, I
Format Journal Article
LanguageEnglish
Published Puerto Rico 01.01.1993
Subjects
Basal Cell Nevus Syndrome - diagnosis
Cerebellar Neoplasms - diagnosis
Follow-Up Studies
Humans
Infant
Male
Medulloblastoma - diagnosis
Neoplasms, Multiple Primary - diagnosis
Skin Neoplasms - diagnosis
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Summary:The basal cell nevus syndrome (BCNS) is a rare autosomal dominant disorder characterized by multiple nevoid basal-cell carcinomas of the skin, recurrent odontogenic keratocysts, skeletal anomalies, developmental malformations, and the predisposition to other neoplastic processes. Among the well known relationships of the syndrome with cancer is that of medulloblastoma. The first known case of BCNS with medulloblastoma in Puerto Rico is presented.
ISSN:0004-4849