Caroli's syndrome: a variable entity

We present the case of a 56 year old woman with Caroli's disease associated to congenital liver fibrosis, renal nephrocalcinosis and cutaneous vasculitis of the legs. Clinical signs of portal hypertension were treated by a shunt technique. After an asymptomatic period, the patient suffers now f...

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Bibliographic Details
Published inRevista española de enfermedades digestivas Vol. 86; no. 5; p. 849
Main Authors Espinosa Aguilar, M D, López de Hierro Ruiz, M, Pinel Julián, L M, González Galilea, A, Suárez Crespo, J F, Ruiz-Cabello, M, Martín-Vivaldi, R
Format Journal Article
LanguageSpanish
Published Spain 01.11.1994
Subjects
Caroli Disease - complications
Caroli Disease - diagnosis
Caroli Disease - therapy
Female
Humans
Middle Aged
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Summary:We present the case of a 56 year old woman with Caroli's disease associated to congenital liver fibrosis, renal nephrocalcinosis and cutaneous vasculitis of the legs. Clinical signs of portal hypertension were treated by a shunt technique. After an asymptomatic period, the patient suffers now from crisis of angiocholitis.
ISSN:1130-0108