Simultaneous repair of cardiovascular disorders and pectus deformity in a patient with Sprintzen-Goldberg syndrome: A case report

We report a 12-year-old girl with Sprintzen-Goldberg syndrome (SGS) who was complicated with annuloaortic ectasia with aortic regurgitation, mitral valve prolapse with mitral regurgitation, and a severe pectus excavatum. In this patient, aortic root replacement, mitral valve replacement, and sternal...

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Bibliographic Details
Published inAnnals of thoracic and cardiovascular surgery Vol. 5; no. 6; p. 411
Main Authors Aoyagi, S, Fukunaga, S, Arinaga, K, Chihara, S, Yokose, S, Sakashita, H, Tobinaga, S, Akashi, H, Kawara, T
Format Journal Article
LanguageEnglish
Published Japan 01.12.1999
Subjects
Aortic Aneurysm - surgery
Aortic Diseases - surgery
Aortic Valve Insufficiency - surgery
Blood Vessel Prosthesis Implantation
Child
Dilatation, Pathologic - surgery
Female
Funnel Chest - surgery
Heart Diseases - surgery
Heart Valve Diseases - surgery
Heart Valve Prosthesis Implantation
Humans
Marfan Syndrome - surgery
Mitral Valve Insufficiency - surgery
Mitral Valve Prolapse - surgery
Sinus of Valsalva - surgery
Sternum - surgery
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Summary:We report a 12-year-old girl with Sprintzen-Goldberg syndrome (SGS) who was complicated with annuloaortic ectasia with aortic regurgitation, mitral valve prolapse with mitral regurgitation, and a severe pectus excavatum. In this patient, aortic root replacement, mitral valve replacement, and sternal elevation were simultaneously performed, and a version of Ravitch's procedure that was technically modified to support the sternum was used for sternal elevation. This modified sternal elevation technique gave excellent operative exposure, and maintained chest wall stability after the operation.
ISSN:1341-1098