다발성 유아기 흑색 신경외배엽성 종양의 치험례

• Published in: Journal of the Korean Association of Oral and Maxillofacial Surgeons Vol. 36; no. 5; pp. 434 - 437
• Main Authors: 최병환(Byoung-Hwan Choi), 박수원(Su-Won Park), 장수미(Soo-Mi Jang), 박봉찬(Bong-Chan Park), 손한나(Han-Na Son), 손장호(Jang-Ho Son), 성일용(Iel-Yong Sung), 김종렬(Jong-Ryoul Kim), 조영철(Yeong-Cheol Cho)
• Format: Journal Article
• Language: Korean
• Published: 대한구강악안면외과학회 30.10.2010; Korean Association Of Oral And Maxillofacial Surgeons
• Subjects: 치의학; Melanotic neuroectodermal tumor of infancy (MNTI); Multicentric
• ISSN: 2234-7550; 2234-5930

A melanotic neuroectodermal tumor of infancy (MNTI) is a uncommon osteolytic pigmented neoplasm that primarily affects the jaws of newborn infants. Most patients (> 90%) present with the tumor in the first year of life. Approximately 65% form in the maxilla, 11% in the mandible, 5% in the brain and elsewhere. MNTI is normally benign, but up to 15% may recur and a few have metastasized. Approximately 200 cases of MNTI have been reported but only 2 of them presented as multifocal. A case of MNTI in a 7 month old boy was encountered. The chief complaint was maxillary anterior ridge swelling. The incisional biopsy findings were MNTI. Two months after the first operation, mild swelling of another site was observed. The infant was examined periodically since undergoing two procedures with no recurrence. This case demonstrates the possibility of a multicentric MNTI. We report a multicentric MNTI with a review of the relevant literature. KCI Citation Count: 0