진균구로 오인된 낭포내 응혈을 보인 23세 여자에서의 선천성 낭포성 유선종 폐기형 1례

• Published in: Tuberculosis and respiratory diseases Vol. 46; no. 1; pp. 129 - 135
• Main Authors: 이강룡, Gang Ryong Lee, 이군순, Kun Sun Lee, 주인규, In Kyu Joo, 박준옥, June Ock Park, 최승준, Seung Jun Choi, 이원석, Won Seok Lee, 김의숙, Eui Sook Kim, 이규현, 김대하, Dae Ha Kim, 이광섭, Gwang Seob Lee, 한영숙, Young Sook Han, 지미경, Mi Ky
• Format: Journal Article
• Language: Korean
• Published: 대한결핵 및 호흡기학회 30.01.1999
• Subjects: CCAM; Fungal ball-like blood clots; Hemorrhage; Hemorrhage; Fungal ball-like blood clots; CCAM
• ISSN: 1738-3536; 2005-6184

We describe unusual manifestations of congenital cystic adenomatoid malformation (C.C.A.M.) of the lung, such as movable fungal ball-like intracystic blood clots and hemoptysis, which were detected in previously healthy 23 years-old woman. We identified blood clots only after left upper lobectomy and could not distinguish from fungal ball with radiographic methods. CCAM of the lung, rare and lethal form of congenital pulmonary cystic disease, was initially introduced by Ch, in and Tang in 1949. The histogenesis of this lesion is characterized by polypoid glandular tissue proliferation and overgrowth of mesenchymal elements due to cessation of bronchiolar maturation which occurred in after 16weeks intrauterine period. In 80-95% of reported cases, the lesion was confined to a single lobe and there was no lobe and right and left lung predilection The clinical presentation may be widely variable, ranging from intrauterine fetal death to late discovery in childhood with recurrent pulmonary infection. But there,s no reports which were misdiagnosed with intracystic fungal ball. The treatment choice is lobectomy of affected lobe. There,s a few case reports with rhabdomyosarcoma, bronchiolar cell carcinoma and myxosarcoma arising in CCAM patients. Therefore, early resection is recommended even if asymtomatic cases. We experienced a rare case of CCAM of the lung in 23 years old female, and there were intracystic fungal ball-like movable blood clots in lower portion of left lung. After left upper lobectomy was performed, now she is discharged and followed up without any complications.