A case of atrial septal aneurysm associated with atrial septal defect
症例は65歳男性で心疾患の既往なし.昭和63年5月より労作時疲労感が出現し通院中の泌尿器科で胸部X線に異常を指摘され当科受診.受診時軽度の心不全状態で,胸部X線上心拡大と肺動脈拡張を,心電図でIRBBB,左房負荷を認めた.心音図で4LSBで汎収縮期雑音を認めた.II音は軽度亢進を認めたが分裂はなかった.断層心エコー図では右室の拡大と卵円窩部に限局する心房中隔瘤を認めた.心房中隔に欠損孔は確認されず,Mモード上心室中隔の奇異性運動も認めなかった.右房造影で瘤は右房内陰影欠損として認められ,右心カテーテルでは肺高血圧(平均肺動脈圧36mmHg)があり,軽度の左右および右左シャントが示唆された。心エ...
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Published in | Shinzo Vol. 23; no. 7; pp. 757 - 762 |
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Main Authors | , , , , , , , , , , , |
Format | Journal Article |
Language | Japanese |
Published |
Japan Heart Foundation
15.07.1991
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Subjects | |
Online Access | Get full text |
ISSN | 0586-4488 2186-3016 |
DOI | 10.11281/shinzo1969.23.7_757 |
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Abstract | 症例は65歳男性で心疾患の既往なし.昭和63年5月より労作時疲労感が出現し通院中の泌尿器科で胸部X線に異常を指摘され当科受診.受診時軽度の心不全状態で,胸部X線上心拡大と肺動脈拡張を,心電図でIRBBB,左房負荷を認めた.心音図で4LSBで汎収縮期雑音を認めた.II音は軽度亢進を認めたが分裂はなかった.断層心エコー図では右室の拡大と卵円窩部に限局する心房中隔瘤を認めた.心房中隔に欠損孔は確認されず,Mモード上心室中隔の奇異性運動も認めなかった.右房造影で瘤は右房内陰影欠損として認められ,右心カテーテルでは肺高血圧(平均肺動脈圧36mmHg)があり,軽度の左右および右左シャントが示唆された。心エコー図上,瘤は通常は左房から右房に突出し,吸気初期には拡張末期,収縮早期に二相性に左房内に反転した.ジギタリス剤,利尿剤による治療約1年後には左房内への反転は減少し右房圧の低下が間接的に示唆された.同時期の2D-ドップラーで瘤の中央から右房に向かう血流が検出された.以上の所見より肺高血圧を伴う二次口型心房中隔欠損症に心房中隔瘤が合併したものと考えた.欠損孔は断層エコーで確認されず,一次中隔の吸収が異常位置で生じ卵円窩部心房中隔が網状となり脆弱性を帯びて瘤が形成されたものと推察した.本例は心房中隔欠損症を伴う心房中隔瘤の発生要因を考えるうえで非常に示唆に富む症例であり瘤の運動パターンの解析および若干の文献的考察を加えた. |
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AbstractList | 症例は65歳男性で心疾患の既往なし.昭和63年5月より労作時疲労感が出現し通院中の泌尿器科で胸部X線に異常を指摘され当科受診.受診時軽度の心不全状態で,胸部X線上心拡大と肺動脈拡張を,心電図でIRBBB,左房負荷を認めた.心音図で4LSBで汎収縮期雑音を認めた.II音は軽度亢進を認めたが分裂はなかった.断層心エコー図では右室の拡大と卵円窩部に限局する心房中隔瘤を認めた.心房中隔に欠損孔は確認されず,Mモード上心室中隔の奇異性運動も認めなかった.右房造影で瘤は右房内陰影欠損として認められ,右心カテーテルでは肺高血圧(平均肺動脈圧36mmHg)があり,軽度の左右および右左シャントが示唆された。心エコー図上,瘤は通常は左房から右房に突出し,吸気初期には拡張末期,収縮早期に二相性に左房内に反転した.ジギタリス剤,利尿剤による治療約1年後には左房内への反転は減少し右房圧の低下が間接的に示唆された.同時期の2D-ドップラーで瘤の中央から右房に向かう血流が検出された.以上の所見より肺高血圧を伴う二次口型心房中隔欠損症に心房中隔瘤が合併したものと考えた.欠損孔は断層エコーで確認されず,一次中隔の吸収が異常位置で生じ卵円窩部心房中隔が網状となり脆弱性を帯びて瘤が形成されたものと推察した.本例は心房中隔欠損症を伴う心房中隔瘤の発生要因を考えるうえで非常に示唆に富む症例であり瘤の運動パターンの解析および若干の文献的考察を加えた. |
Author | Satoh, Yasumasa Akita, Masashi Itoh, Shigenori Takahashi, Yoshitsugu Yazaki, Yutaka Ozeki, Norishige Tanaka, Akitaka Takeuchi, Toshihiko Ogasawara, Tetsuya Itoh, Makoto Takada, Yoshisuke Kojima, Shoji |
Author_FL | 伊藤 重範 Yazaki Yutaka 武内 俊彦 高田 善介 尾関 規重 Ogasawara Tetsuya 小島 照司 佐藤 泰正 高橋 佳嗣 秋田 真志 Tanaka Akitaka 伊藤 誠 |
Author_FL_xml | – sequence: 1 fullname: 伊藤 重範 – sequence: 2 fullname: 高田 善介 – sequence: 3 fullname: 小島 照司 – sequence: 4 fullname: Ogasawara Tetsuya – sequence: 5 fullname: 高橋 佳嗣 – sequence: 6 fullname: Tanaka Akitaka – sequence: 7 fullname: 尾関 規重 – sequence: 8 fullname: Yazaki Yutaka – sequence: 9 fullname: 秋田 真志 – sequence: 10 fullname: 佐藤 泰正 – sequence: 11 fullname: 伊藤 誠 – sequence: 12 fullname: 武内 俊彦 |
Author_xml | – sequence: 1 fullname: Itoh, Shigenori organization: Department of Internal Medicine, Inabe Kosei Hospital – sequence: 1 fullname: Satoh, Yasumasa organization: First Department of Internal Medicine, Nagoya City University School of Medicine – sequence: 1 fullname: Takeuchi, Toshihiko organization: First Department of Internal Medicine, Nagoya City University School of Medicine – sequence: 1 fullname: Ogasawara, Tetsuya organization: Department of Internal Medicine, Inabe Kosei Hospital – sequence: 1 fullname: Tanaka, Akitaka organization: First Department of Internal Medicine, Nagoya City University School of Medicine – sequence: 1 fullname: Yazaki, Yutaka organization: Yazaki Clinic – sequence: 1 fullname: Akita, Masashi organization: First Department of Internal Medicine, Nagoya City University School of Medicine – sequence: 1 fullname: Takahashi, Yoshitsugu organization: Department of Internal Medicine, Inabe Kosei Hospital – sequence: 1 fullname: Ozeki, Norishige organization: Department of Internal Medicine, Inabe Kosei Hospital – sequence: 1 fullname: Takada, Yoshisuke organization: Department of Internal Medicine, Inabe Kosei Hospital – sequence: 1 fullname: Itoh, Makoto organization: First Department of Internal Medicine, Nagoya City University School of Medicine – sequence: 1 fullname: Kojima, Shoji organization: Department of Internal Medicine, Inabe Kosei Hospital |
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References | 3) Lev M: Autopsy diagnosis of congenitally malformed hearts. Springfield, III, Charles C Thomas, 1953, pp 22-23 4) Casta A: Atrial septal aneurysm herniation across the mitral valve orifice in pulmonary atresia. Am Heart J 115: 1136-1138, 1988 6) Gallet B, Malergue MC, Adams C, et al: Atrial septal aneurysm-a potential cause of systemic embolism An echocardiographic study. Br Heart J 53: 292-297, 1985 9) Kondo T, Iwasaki T, Hiramatsu K, et al: Partial Resection of Atrial Septal Aneurysm with Multiple Fenestrations-A Case Report. Angiology 39: 838-842, 1988 8) Kong C-W and Chan W: The Echocardiographic Features of an Aneurysm of the Inter-Atrial Septum. Angiology 35: 188-194, 1984 5) Iliceto S, Papa A, Sorino M, et al: Combined Atrial Septal Aneurysm and Mitral Valve Prolapse: Detection by Two-Dimensional Echocardiography. Am J Cardiol 54: 1151-1153, 1984 2) Hanley PC, Tajik AJ, Hynes JK, et al: Diagnosis and Classification of Atrial Septal Aneurysm by Two-Dimensional Echocardiography: Report of 80 Consecutive Cases. JACC 6: 1370 -1382, 1985 7) Belkin RN, Hurwitz BJ and Kisslo J: Atrial Septal Aneurysm: Association with Cerebrovascular and Peripheral Embolic Events. Stroke 18: 856-862, 1987 1) Silver MD and Dorsey JS: Aneurysms of the Septum Primum in Adults. Arch Pathol Lab Med 102: 62-65, 1978 10)松岡優, 中沢誠: 心房中隔欠損. 臨床発達心臓病学. 高尾篤良編, 東京, 中外医学社, 1989, pp232-233 |
References_xml | – reference: 4) Casta A: Atrial septal aneurysm herniation across the mitral valve orifice in pulmonary atresia. Am Heart J 115: 1136-1138, 1988 – reference: 7) Belkin RN, Hurwitz BJ and Kisslo J: Atrial Septal Aneurysm: Association with Cerebrovascular and Peripheral Embolic Events. Stroke 18: 856-862, 1987 – reference: 10)松岡優, 中沢誠: 心房中隔欠損. 臨床発達心臓病学. 高尾篤良編, 東京, 中外医学社, 1989, pp232-233 – reference: 8) Kong C-W and Chan W: The Echocardiographic Features of an Aneurysm of the Inter-Atrial Septum. Angiology 35: 188-194, 1984 – reference: 1) Silver MD and Dorsey JS: Aneurysms of the Septum Primum in Adults. Arch Pathol Lab Med 102: 62-65, 1978 – reference: 5) Iliceto S, Papa A, Sorino M, et al: Combined Atrial Septal Aneurysm and Mitral Valve Prolapse: Detection by Two-Dimensional Echocardiography. Am J Cardiol 54: 1151-1153, 1984 – reference: 9) Kondo T, Iwasaki T, Hiramatsu K, et al: Partial Resection of Atrial Septal Aneurysm with Multiple Fenestrations-A Case Report. Angiology 39: 838-842, 1988 – reference: 2) Hanley PC, Tajik AJ, Hynes JK, et al: Diagnosis and Classification of Atrial Septal Aneurysm by Two-Dimensional Echocardiography: Report of 80 Consecutive Cases. JACC 6: 1370 -1382, 1985 – reference: 3) Lev M: Autopsy diagnosis of congenitally malformed hearts. Springfield, III, Charles C Thomas, 1953, pp 22-23 – reference: 6) Gallet B, Malergue MC, Adams C, et al: Atrial septal aneurysm-a potential cause of systemic embolism An echocardiographic study. Br Heart J 53: 292-297, 1985 |
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Title | A case of atrial septal aneurysm associated with atrial septal defect |
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