MRIにて動眼神経圧迫を確認し得た下垂体炎に伴う下垂体卒中の56歳男性例

症例は56歳男性である.突然の頭痛,発熱,瞳孔異常を伴わない右動眼神経麻痺,意識障害で発症した.頭部MRIでT1高信号を伴う下垂体の腫大より下垂体卒中と診断した.下垂体前葉ホルモンの著明な低下と中枢性尿崩症を呈したため高用量ステロイドを開始し,2日後に意識障害と頭痛は改善した.第30病日のMRIで腫瘤の明らかな縮小と動眼神経圧迫の改善を認めた.ステロイドへの迅速な反応と下垂体病変の消失から,下垂体卒中の原因は下垂体炎と推察した.頭部thin slice MRIで海面静脈洞入口部における動眼神経圧迫を認め,動眼神経麻痺の病態として栄養血管の血流障害を考えた....

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Published in臨床神経学 Vol. 58; no. 11; pp. 668 - 672
Main Authors 櫻井, 慎太郎, 五十嵐, 晴紀, 平田, 幸一, 国分, 則人, 舩越, 慶
Format Journal Article
LanguageJapanese
Published 日本神経学会 2018
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ISSN0009-918X
1882-0654
DOI10.5692/clinicalneurol.cn-001192

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Abstract 症例は56歳男性である.突然の頭痛,発熱,瞳孔異常を伴わない右動眼神経麻痺,意識障害で発症した.頭部MRIでT1高信号を伴う下垂体の腫大より下垂体卒中と診断した.下垂体前葉ホルモンの著明な低下と中枢性尿崩症を呈したため高用量ステロイドを開始し,2日後に意識障害と頭痛は改善した.第30病日のMRIで腫瘤の明らかな縮小と動眼神経圧迫の改善を認めた.ステロイドへの迅速な反応と下垂体病変の消失から,下垂体卒中の原因は下垂体炎と推察した.頭部thin slice MRIで海面静脈洞入口部における動眼神経圧迫を認め,動眼神経麻痺の病態として栄養血管の血流障害を考えた.
AbstractList 症例は56歳男性である.突然の頭痛,発熱,瞳孔異常を伴わない右動眼神経麻痺,意識障害で発症した.頭部MRIでT1高信号を伴う下垂体の腫大より下垂体卒中と診断した.下垂体前葉ホルモンの著明な低下と中枢性尿崩症を呈したため高用量ステロイドを開始し,2日後に意識障害と頭痛は改善した.第30病日のMRIで腫瘤の明らかな縮小と動眼神経圧迫の改善を認めた.ステロイドへの迅速な反応と下垂体病変の消失から,下垂体卒中の原因は下垂体炎と推察した.頭部thin slice MRIで海面静脈洞入口部における動眼神経圧迫を認め,動眼神経麻痺の病態として栄養血管の血流障害を考えた.
Author 舩越, 慶
五十嵐, 晴紀
国分, 則人
平田, 幸一
櫻井, 慎太郎
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References 1) Reid RL, Quigley ME, Yen SSC, et al. Pituitary apoplexy: a review. Arch Neurol 1985;42:712-719.
16) Davies EC, Jakobiec FA, Stagner DAM, et al. An atypical case of lymphocytic panhypophysitis in a pregnant woman. J Neuroophthalmol 2016;36:313-316.
14) Husain Q, Zouzias A, Kanumuri V, et al. Idiopatic granulomatous hypophysitis presenting as pituitary apoplexy. J Clin Neurosci 2014;21:510-512.
11) Tonda C, Rizvi AA. Headache, pituitary lesion and panhypopituitarism in a pregnant woman: tumor, apoplexy or hypophysitis? Am J Med Sci 2011;342:247-249.
2) Boellis A, Napoli AD, Romano A, et al. Pituitary apoplexy an update on clinical and imaging features. Insights Imaging 2014;5:753-762.
13) Tanaka Y, Hirao T, Tsutsumi K, et al. A case of apoplectic lymphocytic hypophysitis complicated by polymyalgia rheumatic. Rheumatol Int 2013;33:215-218.
15) Sellayah R, Gonzales M, Fourlanos S, et al. Lymphocytic hypophysitis in the elderly. J Clin Neurosci 2015;22:1842-1843.
5) Semple PL, Jane JA, Lopes MBS, et al. Pituitary apoplexy: correlation between magnetic resonance imaging and histopathological results. J Neurosurg 2008;108:909-915.
10) Minakshi B, Alok S, Hillol K. Lymphocytic hypophysitis presenting as pituitary apoplexy in a male. Neurology India 2005;53:363-364.
17) Yuen KCJ, Moloney KJ, Mercado JU, et al. A case series of atypical features of patients with biopsy-proven isolated IgG4-related hypophysitis and normal serum IgG4 levels. Pituitary 2018;21:238-246.
6) 大磯ユタカ.自己免疫性視床下部下垂体炎の診断と治療の手引き(平成21年度改訂).厚生労働科学研究費補助金難治性疾患克服研究事業,間脳下垂体機能障害に関する調査研究班.平成21年度総括・分担研究報告書.2010. P. 162-165.
12) Gutenberg A, Caturegli P, Metz I, et al. Necrotizing infundibulo-hypophysitis: an entity too rare to be true? Pituitary 2012;15:202-208.
3) Glezer A, Bronstein MD. Pituitary apoplexy pathophysiology, diagnosis and management. Arch Endocrinol Metab 2015;59:259-264.
9) Lee MS, Pless M. Apoplectic lymphocytic hypophysitis. Case report. J Neurosurg 2003;98:183-185.
7) 佐々木悠,大西 修,前原史明ら.下垂体卒中を契機に,下垂体前葉機能低下症,中枢性尿崩症に加え,一過性甲状腺中毒症(painless thyroiditis)を呈した症例とその病態について.日内分泌会誌 1990;66:9-21.
8) Dan NG, Feiner RID, Houang MTW, et al. Pituitary apoplexy in association with lymphocytic hypophysitis. J Clin Neurosci 2002;9:577-580.
18) 有馬 寛.下垂体後葉.日内分泌会誌 2012;101:924-928.
19) Kobayashi H, Kawabori M, Terasaka S, et al. A possible mechanism of isolated oculomotor nerve palsy by apoplexy of pituitary adenoma without cavernous sinus invasion a report of two cases. Acta Neurochir 2011;153:2453-2456.
4) Briet C, Salenave S, Bonneville J, et al. Pituitary apoplexy. Endocrine Rev 2015;36:622-645.
References_xml – reference: 8) Dan NG, Feiner RID, Houang MTW, et al. Pituitary apoplexy in association with lymphocytic hypophysitis. J Clin Neurosci 2002;9:577-580.
– reference: 12) Gutenberg A, Caturegli P, Metz I, et al. Necrotizing infundibulo-hypophysitis: an entity too rare to be true? Pituitary 2012;15:202-208.
– reference: 4) Briet C, Salenave S, Bonneville J, et al. Pituitary apoplexy. Endocrine Rev 2015;36:622-645.
– reference: 7) 佐々木悠,大西 修,前原史明ら.下垂体卒中を契機に,下垂体前葉機能低下症,中枢性尿崩症に加え,一過性甲状腺中毒症(painless thyroiditis)を呈した症例とその病態について.日内分泌会誌 1990;66:9-21.
– reference: 17) Yuen KCJ, Moloney KJ, Mercado JU, et al. A case series of atypical features of patients with biopsy-proven isolated IgG4-related hypophysitis and normal serum IgG4 levels. Pituitary 2018;21:238-246.
– reference: 1) Reid RL, Quigley ME, Yen SSC, et al. Pituitary apoplexy: a review. Arch Neurol 1985;42:712-719.
– reference: 14) Husain Q, Zouzias A, Kanumuri V, et al. Idiopatic granulomatous hypophysitis presenting as pituitary apoplexy. J Clin Neurosci 2014;21:510-512.
– reference: 6) 大磯ユタカ.自己免疫性視床下部下垂体炎の診断と治療の手引き(平成21年度改訂).厚生労働科学研究費補助金難治性疾患克服研究事業,間脳下垂体機能障害に関する調査研究班.平成21年度総括・分担研究報告書.2010. P. 162-165.
– reference: 2) Boellis A, Napoli AD, Romano A, et al. Pituitary apoplexy an update on clinical and imaging features. Insights Imaging 2014;5:753-762.
– reference: 16) Davies EC, Jakobiec FA, Stagner DAM, et al. An atypical case of lymphocytic panhypophysitis in a pregnant woman. J Neuroophthalmol 2016;36:313-316.
– reference: 9) Lee MS, Pless M. Apoplectic lymphocytic hypophysitis. Case report. J Neurosurg 2003;98:183-185.
– reference: 3) Glezer A, Bronstein MD. Pituitary apoplexy pathophysiology, diagnosis and management. Arch Endocrinol Metab 2015;59:259-264.
– reference: 5) Semple PL, Jane JA, Lopes MBS, et al. Pituitary apoplexy: correlation between magnetic resonance imaging and histopathological results. J Neurosurg 2008;108:909-915.
– reference: 13) Tanaka Y, Hirao T, Tsutsumi K, et al. A case of apoplectic lymphocytic hypophysitis complicated by polymyalgia rheumatic. Rheumatol Int 2013;33:215-218.
– reference: 11) Tonda C, Rizvi AA. Headache, pituitary lesion and panhypopituitarism in a pregnant woman: tumor, apoplexy or hypophysitis? Am J Med Sci 2011;342:247-249.
– reference: 15) Sellayah R, Gonzales M, Fourlanos S, et al. Lymphocytic hypophysitis in the elderly. J Clin Neurosci 2015;22:1842-1843.
– reference: 18) 有馬 寛.下垂体後葉.日内分泌会誌 2012;101:924-928.
– reference: 19) Kobayashi H, Kawabori M, Terasaka S, et al. A possible mechanism of isolated oculomotor nerve palsy by apoplexy of pituitary adenoma without cavernous sinus invasion a report of two cases. Acta Neurochir 2011;153:2453-2456.
– reference: 10) Minakshi B, Alok S, Hillol K. Lymphocytic hypophysitis presenting as pituitary apoplexy in a male. Neurology India 2005;53:363-364.
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SubjectTerms 下垂体卒中
下垂体炎
動眼神経
海面静脈洞
Title MRIにて動眼神経圧迫を確認し得た下垂体炎に伴う下垂体卒中の56歳男性例
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