後腹膜脂肪肉腫を疑った多発仙骨前面骨髄脂肪腫の1例

症例は72歳,女性.鼠径部粉瘤の精査の際に,腹部CTを施行したところ後腹膜,仙骨前面に腫瘤を指摘されたため,当科受診をした.腹部CTで骨盤内に66mm,48mm,10mm大の腫瘤性病変を認めた.遠隔転移を認めなかったが,多発性腫瘤であり悪性度が高いと判断し,後腹膜脂肪肉腫の疑いとして開腹腫瘤摘出術を施行した.病理診断の結果は副腎外骨髄脂肪腫であり,仙骨前面骨髄脂肪腫と診断した.術後4年7カ月現在,無再発生存中である.多発性の副腎外骨髄脂肪腫は本邦では報告例はない.今回,われわれは稀な症例を経験したので報告する....

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Published in日本臨床外科学会雑誌 Vol. 83; no. 4; pp. 780 - 784
Main Authors 久留宮, 康浩, 加藤, 健宏, 世古口, 英, 菅原, 元, 井上, 昌也, 関本, 晃裕
Format Journal Article
LanguageJapanese
Published 日本臨床外科学会 2022
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ISSN1345-2843
1882-5133
DOI10.3919/jjsa.83.780

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Abstract 症例は72歳,女性.鼠径部粉瘤の精査の際に,腹部CTを施行したところ後腹膜,仙骨前面に腫瘤を指摘されたため,当科受診をした.腹部CTで骨盤内に66mm,48mm,10mm大の腫瘤性病変を認めた.遠隔転移を認めなかったが,多発性腫瘤であり悪性度が高いと判断し,後腹膜脂肪肉腫の疑いとして開腹腫瘤摘出術を施行した.病理診断の結果は副腎外骨髄脂肪腫であり,仙骨前面骨髄脂肪腫と診断した.術後4年7カ月現在,無再発生存中である.多発性の副腎外骨髄脂肪腫は本邦では報告例はない.今回,われわれは稀な症例を経験したので報告する.
AbstractList 症例は72歳,女性.鼠径部粉瘤の精査の際に,腹部CTを施行したところ後腹膜,仙骨前面に腫瘤を指摘されたため,当科受診をした.腹部CTで骨盤内に66mm,48mm,10mm大の腫瘤性病変を認めた.遠隔転移を認めなかったが,多発性腫瘤であり悪性度が高いと判断し,後腹膜脂肪肉腫の疑いとして開腹腫瘤摘出術を施行した.病理診断の結果は副腎外骨髄脂肪腫であり,仙骨前面骨髄脂肪腫と診断した.術後4年7カ月現在,無再発生存中である.多発性の副腎外骨髄脂肪腫は本邦では報告例はない.今回,われわれは稀な症例を経験したので報告する.
Author 世古口, 英
加藤, 健宏
久留宮, 康浩
井上, 昌也
菅原, 元
関本, 晃裕
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References 7) Tokuyama N, Takeuchi H, Kuroda I, et al : Incidental presacral myelolipoma resembling the liposarcoma : A case report and literature review. Case Rep Urol 2016 ; 2016 : 6510930.doi : 10.1155/2016/6510930
14) Andriandi, Cleven AHG, Hanff DF, et al : Presacral myelolipoma, case report and literature review. Ann Med Surg(Lond) 2020 ; 57 : 274-280
5) Dodge OG, Evans DM : Haemopoiesis in a presacral fatty tumor (myelolipoma). J Pathol Bacteriol 1956 ; 72 : 313-317
2) Singla AK, Kechejian G, Lopez MJ : Giant presacral myelolipoma. Am Surg 2003 ; 69 : 334-338
12) Rizzo G, Coramusi C, Pietricola G, et al : Laparoscopic approach for a presacral myelolipoma resembling a liposarcoma. J Surg Case Rep 2018 ; 2018 : rjy156.doi : 10.1093/jscr/rjy156
3) Shin NY, Kim MJ, Chung JJ, et al : The differential imaging features of fat-containing tumors in the peritoneal cavity and retroperitoneum : the radiologic-pathologic correlation. Korean J Radiol 2010 ; 11 : 333-345
16) Baker KS, Lee D, Huang M, et al : Presacral myelolipoma : a case report and review of imaging findings. J Radiol Case Rep 2012 ; 6 : 1-9
13) Sethi S, Thakur S, Jacques S, et al : Myelolipoma of the pelvis : A case report and review of literature. Front Oncol 2018 ; 8 : 251.doi : 10.3389/fonc.2018.00251
15) Gill KR, Hasan MK, Menke DM, et al : Presacral myelolipoma : diagnosis by EUS-FNA and Trucut biopsy. Gastrointest Endosc 2010 ; 71 : 849-850
6) 上江洌一平,南 一仁,松山純子他:仙骨前面骨髄脂肪腫の1例.日消外会誌 2017;50:158-165
11) Sakamoto A, Nagamatsu I, Shiba E, et al : Presacral myelolipoma as a possible parasymptom of cancer : A case report. Rare Tumors 2018 ; 10 : 2036361318772124. doi : 10.1177/2036361318772124
10) Cho MH, Mandaliya R, Liang J, et al : A case report of symptomatic presacral myelolipoma. Medicine(Baltimore)2018 ; 97 : e0337.doi : 10.1097/MD.0000000000010337
8) Lee JJ, Dickson BC, Sreeharsha B, et al : Presacral myelolipoma : diagnosis on imaging with pathologic and clinical correlation. AJR Am J Roentgenol 2016 ; 207 : 470-481
4) 那須啓一,志田 大,松岡勇二郎他:仙骨前面骨髄脂肪腫の1例.日消外会誌 2011;44:1485-1492
1) Olsson CA, Krane RJ, Klugo RC, et al : Adrenal myelolipoma. Surgery 1973 ; 73 : 665-670
9) Arora K, Sidhu J : Extra-adrenal myelolipoma containing small lymphocytic lymphoma/chronic lymphocytic leukemia : A case report and review of the literature. Case Rep Hematol 2016 ; 2016 : 7364951. doi : 10.1155/2016/7364951
References_xml – reference: 12) Rizzo G, Coramusi C, Pietricola G, et al : Laparoscopic approach for a presacral myelolipoma resembling a liposarcoma. J Surg Case Rep 2018 ; 2018 : rjy156.doi : 10.1093/jscr/rjy156
– reference: 1) Olsson CA, Krane RJ, Klugo RC, et al : Adrenal myelolipoma. Surgery 1973 ; 73 : 665-670
– reference: 5) Dodge OG, Evans DM : Haemopoiesis in a presacral fatty tumor (myelolipoma). J Pathol Bacteriol 1956 ; 72 : 313-317
– reference: 11) Sakamoto A, Nagamatsu I, Shiba E, et al : Presacral myelolipoma as a possible parasymptom of cancer : A case report. Rare Tumors 2018 ; 10 : 2036361318772124. doi : 10.1177/2036361318772124
– reference: 4) 那須啓一,志田 大,松岡勇二郎他:仙骨前面骨髄脂肪腫の1例.日消外会誌 2011;44:1485-1492
– reference: 2) Singla AK, Kechejian G, Lopez MJ : Giant presacral myelolipoma. Am Surg 2003 ; 69 : 334-338
– reference: 9) Arora K, Sidhu J : Extra-adrenal myelolipoma containing small lymphocytic lymphoma/chronic lymphocytic leukemia : A case report and review of the literature. Case Rep Hematol 2016 ; 2016 : 7364951. doi : 10.1155/2016/7364951
– reference: 13) Sethi S, Thakur S, Jacques S, et al : Myelolipoma of the pelvis : A case report and review of literature. Front Oncol 2018 ; 8 : 251.doi : 10.3389/fonc.2018.00251
– reference: 14) Andriandi, Cleven AHG, Hanff DF, et al : Presacral myelolipoma, case report and literature review. Ann Med Surg(Lond) 2020 ; 57 : 274-280
– reference: 8) Lee JJ, Dickson BC, Sreeharsha B, et al : Presacral myelolipoma : diagnosis on imaging with pathologic and clinical correlation. AJR Am J Roentgenol 2016 ; 207 : 470-481
– reference: 10) Cho MH, Mandaliya R, Liang J, et al : A case report of symptomatic presacral myelolipoma. Medicine(Baltimore)2018 ; 97 : e0337.doi : 10.1097/MD.0000000000010337
– reference: 15) Gill KR, Hasan MK, Menke DM, et al : Presacral myelolipoma : diagnosis by EUS-FNA and Trucut biopsy. Gastrointest Endosc 2010 ; 71 : 849-850
– reference: 3) Shin NY, Kim MJ, Chung JJ, et al : The differential imaging features of fat-containing tumors in the peritoneal cavity and retroperitoneum : the radiologic-pathologic correlation. Korean J Radiol 2010 ; 11 : 333-345
– reference: 7) Tokuyama N, Takeuchi H, Kuroda I, et al : Incidental presacral myelolipoma resembling the liposarcoma : A case report and literature review. Case Rep Urol 2016 ; 2016 : 6510930.doi : 10.1155/2016/6510930
– reference: 6) 上江洌一平,南 一仁,松山純子他:仙骨前面骨髄脂肪腫の1例.日消外会誌 2017;50:158-165
– reference: 16) Baker KS, Lee D, Huang M, et al : Presacral myelolipoma : a case report and review of imaging findings. J Radiol Case Rep 2012 ; 6 : 1-9
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SubjectTerms 仙骨前面
多発
骨髄脂肪腫
Title 後腹膜脂肪肉腫を疑った多発仙骨前面骨髄脂肪腫の1例
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