A surgical report of Bland White Garland syndrome

• Published in: Annals of thoracic and cardiovascular surgery Vol. 15; no. 1; pp. 53 - 57
• Main Authors: Akhtar, Raja Parvez, Waheed, Abdul, Abid, Abdul Rehman, Mohyuddin, Muhammad Tahir, Faruqui, Zia, Khan, Jawad Sajid
• Format: Journal Article
• Language: English
• Published: Japan 01.02.2009
• Subjects: Angina Pectoris - etiology; Aorta - surgery; Cardiac Surgical Procedures; Cardiopulmonary Bypass; Coronary Angiography; Coronary Vessel Anomalies - complications; Coronary Vessel Anomalies - pathology; Coronary Vessel Anomalies - physiopathology; Coronary Vessel Anomalies - surgery; Echocardiography, Transesophageal; Female; Hemodynamics; Humans; Pericardium - transplantation; Pulmonary Artery - abnormalities; Pulmonary Artery - pathology; Pulmonary Artery - physiopathology; Pulmonary Artery - surgery; Replantation; Syndrome; Tomography, X-Ray Computed; Treatment Outcome; Young Adult
• ISSN: 2186-1005

We report a 22-year-old mother of 2 who presented to us with exertional chest pain for 3 years. On coronary angiography she was diagnosed to be suffering from Bland White Garland syndrome (BWGS). She had a giant and grossly tortuous right coronary artery (RCA) forming collaterals with the left coronary artery (LCA), which was draining into the pulmonary artery (PA). Surprisingly, she had no evidence of mitral regurgitation on echocardiography, and she had a preserved left ventricular systolic function. She underwent Takeuchi's repair with uneventful recovery. Postoperative CT angiography revealed adequate reimplantation of the left main coronary artery to the aorta with patent tunnel. On a 6-month follow-up, she is asymptomatic and has an optimal flow through the tunnel to the LCA.