FAMILIAL HYPERTROPHIC CARDIOMYOPATHY MIMICING TYPICAL DILATED CARDIOMYOPATHY

This paper reports on two patients with symptomatic familial hypertrophic cardiomy-opathy, who presented with congestive heart failure and a dilated left ventricle (LV). Case 1: A 37-year-old male was admitted on 16 May 1988, because of acute pulmonary edema. Subsequent echocardiographic examination...

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Bibliographic Details
Published inJapanese Journal of National Medical Services Vol. 44; no. 9; pp. 927 - 930
Main Authors EJIRI, Nariaki, MITSUHASHI, Takeshi, KOKAJI, Kiyokazu, SHIN, Hankei, YOSHIDA, Yasuhiro, IKEJIRI, Koji
Format Journal Article
LanguageJapanese
Published Japanese Society of National Medical Services 1990
Subjects
dilated cardiomyopathy
familial cardiomy-opathy
hypertrophic cardiomyopathy
myocardial disarray
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Summary:This paper reports on two patients with symptomatic familial hypertrophic cardiomy-opathy, who presented with congestive heart failure and a dilated left ventricle (LV). Case 1: A 37-year-old male was admitted on 16 May 1988, because of acute pulmonary edema. Subsequent echocardiographic examinations revealed LV dilatation, generalized LV hypokinesis and asymmetrical septal hypertrophy. Right ventricular (RV) endocardial biopsy findings showed moderate myocardial disarray and hypertrophy as found in hyper-trophic cardiomyopathy (HCM). Case 2: A 35-year-old male was admitted on 15 Feb. 1988, because of palpitation. His electrocardiography showed WPW (type A) pattern. His echocardiography showed LV dilatation and generalized hypokinesis. RV biopsy show-ed mild myocardial disarray as found in Case 1. We conclude that these two cases might progress from the state of hypertrophic cardiomyopathy to dilated cardiomyopathy-like features.
ISSN:0021-1699
1884-8729
DOI:10.11261/iryo1946.44.927