膵管癒合不全に合併した膵管内乳頭粘液性腫瘍に対して尾側膵亜全摘を行った1例
症例は74歳の女性で,膵炎の診断で前医入院加療された際に膵管内乳頭粘液性腫瘍(intraductal papillary mucinous neoplasm;以下,IPMNと略記)を指摘され当院紹介となった.ERCPを含む画像精査にて膵管癒合不全を認め,Santorini管はびまん性の拡張を認めた.拡張膵管内に明らかな壁在結節は指摘されず,膵液細胞診はClass IIIであった.検査で浸潤癌を示唆する所見がないこと,膵管癒合不全を認めること,かつ膵管拡張がSantorini管に限局していたことから,背側膵に限局した混合型IPMNと診断し腹側膵を温存した尾側膵亜全摘術を行った.術後に膵液瘻を認め...
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Published in | 日本消化器外科学会雑誌 Vol. 55; no. 12; pp. 758 - 764 |
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Main Authors | , , , , , , , , , , |
Format | Journal Article |
Language | Japanese |
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一般社団法人 日本消化器外科学会
01.12.2022
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ISSN | 0386-9768 1348-9372 |
DOI | 10.5833/jjgs.2021.0163 |
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Abstract | 症例は74歳の女性で,膵炎の診断で前医入院加療された際に膵管内乳頭粘液性腫瘍(intraductal papillary mucinous neoplasm;以下,IPMNと略記)を指摘され当院紹介となった.ERCPを含む画像精査にて膵管癒合不全を認め,Santorini管はびまん性の拡張を認めた.拡張膵管内に明らかな壁在結節は指摘されず,膵液細胞診はClass IIIであった.検査で浸潤癌を示唆する所見がないこと,膵管癒合不全を認めること,かつ膵管拡張がSantorini管に限局していたことから,背側膵に限局した混合型IPMNと診断し腹側膵を温存した尾側膵亜全摘術を行った.術後に膵液瘻を認めたが保存的に閉鎖し,術後42日で退院となった.病理診断はlow grade IPMNであり悪性所見は認めなかった.膵管癒合不全に生じたIPMNに対して,腹側膵を温存した切除例の報告はまれであり報告する. |
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AbstractList | 症例は74歳の女性で,膵炎の診断で前医入院加療された際に膵管内乳頭粘液性腫瘍(intraductal papillary mucinous neoplasm;以下,IPMNと略記)を指摘され当院紹介となった.ERCPを含む画像精査にて膵管癒合不全を認め,Santorini管はびまん性の拡張を認めた.拡張膵管内に明らかな壁在結節は指摘されず,膵液細胞診はClass IIIであった.検査で浸潤癌を示唆する所見がないこと,膵管癒合不全を認めること,かつ膵管拡張がSantorini管に限局していたことから,背側膵に限局した混合型IPMNと診断し腹側膵を温存した尾側膵亜全摘術を行った.術後に膵液瘻を認めたが保存的に閉鎖し,術後42日で退院となった.病理診断はlow grade IPMNであり悪性所見は認めなかった.膵管癒合不全に生じたIPMNに対して,腹側膵を温存した切除例の報告はまれであり報告する. |
Author | 仁熊, 健文 熊野, 健二郎 櫻井, 湧哉 三宅, 英輝 片山, 哲也 児島, 亨 成田, 周平 岡, 凌也 梶岡, 裕紀 藤, 智和 能勢, 聡一郎 |
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References | 4) 大池 信之,国村 利明,榎澤 哲司,田所 賢也,石川 祐輔,宮坂 信雄,ほか.【膵管癒合不全(divisum)―その臨床的意義をめぐって】膵管癒合不全(膵divisum)発生と解剖.胆と膵.1997;18(9):813–819. 19) Tanaka M, Fernández-Del Castillo C, Kamisawa T, Jang JY, Levy P, Ohtsuka T, et al. Revisions of international consensus Fukuoka guidelines for the management of IPMN of the pancreas. Pancreatology. 2017;17:738–753. 16) Di Mitri R, Scimeca D, Conte E, Unti E, Mocciaro F. Mixed-type intraductal papillary mucinous neoplasm in a patient with pancreas divisum: pancreatoscopy through the Santorini duct with direct intraductal biopsy. Gastrointest Endosc. 2020;91(6):1398–1400. 12) Scatton O, Sauvanet A, Cazals-Hatem D, Vullierme MP, Ruszniewski P, Belghiti J. Dorsal pancreatectomy: an embryology-based resection. J Gastrointest Surg. 2006;10(3):434–438. 20) 竹山 宜典.【IPMN・MCN国際診療ガイドライン総まとめ】主膵管型IPMNの手術適応と術式.胆と膵.2020;41(1):37–40. 5) Warshaw AL, Simeone JF, Schapiro RH, Flavin-Warshaw B. Evaluation and treatment of the dominant dorsal duct syndrome (pancreas divisum redefined). Am J Surg. 1990;159(1):59–64; discussion -6. 11) Akizuki E, Kimura Y, Mukaiya M, Honnma T, Koito K, Katsuramaki T, et al. A case of intraductal papillary mucinous tumor associated with pancreas divisum. Pancreas. 2006;32(1):117–118. 8) Sakurai Y, Matsubara T, Imazu H, Hasegawa S, Miyakawa S, Ochiai M, et al. Intraductal papillary-mucinous tumor of the pancreas head with complete absence of the ventral pancreatic duct of Wirsung. J Hepatobiliary Pancreat Surg. 2004;11(4):293–298. 23) 村上 義昭,上村 健一郎,近藤 成,中川 直哉,岡野 圭介,岡田 健司郎,ほか.【膵内・外分泌機能をめぐる現状と展望】膵切除術における機能温存の考え方.膵臓.2017;32(4):706–713. 1) Hayakawa T, Kondo T, Shibata T, Sugimoto Y, Kitagawa M, Suzuki T, et al. Pancreas divisum. A predisposing factor to pancreatitis? Int J Pancreatol. 1989;5(4):317–326. 17) Dickson ZA, Sauer BG. Intraductal papillary mucinous neoplasm of the pancreas associated with pancreas divisum resulting in a “fish-eye” minor papilla. Gastrointest Endosc. 2020;91(6):1396–1397. 15) Baiocco JA, Ackerman CT, Crawford JL, Yeo CJ. Intraductal papillary mucinous neoplasm and pancreas divisum: two cases. J Pancreat Cancer. 2016;2(1):28–31. 14) Nishi T, Kawabata Y, Ishikawa N, Araki A, Yano S, Maruyama R, et al. Intraductal papillary mucinous carcinoma of the pancreas associated with pancreas divisum: a case report and review of the literature. BMC Gastroenterol. 2015;15:78. 9) Sakate Y, Ohira M, Maeda K, Yamada N, Nishihara T, Nakata B, et al. Intraductal papillary-mucinous adenoma developed in the ventral pancreas in a patient with pancreas divisum. J Hepatobiliary Pancreat Surg. 2004;11(5):366–370. 18) Ardengh JC, Taglieri E, Ardengh AO, De Almeida AF, Surjan RC, Makdissi F, et al. Intraoperative SpyGlass to determine extension of pancreatic resection in main duct intraductal papillary mucinous neoplasm associated with pancreas divisum. Endoscopy. 2021;53(5):E191–3. 22) 須藤 広誠,岡野 圭一,鈴木 康之.膵切除後の膵性糖尿病について.膵臓.2019;34(4):166–171. 6) Thayer SP, Fernández-del Castillo C, Balcom JH, Warshaw AL. Complete dorsal pancreatectomy with preservation of the ventral pancreas: a new surgical technique. Surgery. 2002;131(5):577–580. 21) 庭野 史丸,馬場谷 成,廣峰 義久,池上 博司.【膵全摘術を考える】膵全摘術後の膵内分泌機能異常(病態と治療).胆と膵.2019;40(1):75–79. 3) 岡田 純,上坂 克彦,森本 剛史,小寺 泰弘,鳥井 彰人,平井 孝,ほか.膵管癒合不全の背側膵に発生した膵頭部癌の1例.日本消化器外科学会雑誌.1996;29(4):843–847. 7) Yarze JC, Chase MP, Herlihy KJ, Nawras A. Pancreas divisum and intraductal papillary mucinous tumor occurring simultanously in a patient presenting with recurrent acute pancreatitis. Dig Dis Sci. 2003;48(5):915. 13) Gurram KC, Czapla A, Thakkar S. Acute pancreatitis: pancreas divisum with ventral duct intraductal papillary mucinous neoplasms. BMJ Case Rep. 2014 Oct;2014:bcr2014205322. 10) Talbot ML, Foulis AK, Imrie CW. Total dorsal pancreatectomy for intraductal papillary mucinous neoplasm in a patient with pancreas divisum. Pancreatology. 2005;5(2–3):285–288. 2) Cotton PB. Congenital anomaly of pancreas divisum as cause of obstructive pain and pancreatitis. Gut. 1980;21(2):105–114. 24) 東原 琢,吉富 秀幸,清水 宏明,大塚 将之,加藤 厚,古川 勝規,ほか.中央区域温存膵切除術の4例.日本消化器外科学会雑誌.2016;49(5):439–446. |
References_xml | – reference: 1) Hayakawa T, Kondo T, Shibata T, Sugimoto Y, Kitagawa M, Suzuki T, et al. Pancreas divisum. A predisposing factor to pancreatitis? Int J Pancreatol. 1989;5(4):317–326. – reference: 4) 大池 信之,国村 利明,榎澤 哲司,田所 賢也,石川 祐輔,宮坂 信雄,ほか.【膵管癒合不全(divisum)―その臨床的意義をめぐって】膵管癒合不全(膵divisum)発生と解剖.胆と膵.1997;18(9):813–819. – reference: 7) Yarze JC, Chase MP, Herlihy KJ, Nawras A. Pancreas divisum and intraductal papillary mucinous tumor occurring simultanously in a patient presenting with recurrent acute pancreatitis. Dig Dis Sci. 2003;48(5):915. – reference: 12) Scatton O, Sauvanet A, Cazals-Hatem D, Vullierme MP, Ruszniewski P, Belghiti J. Dorsal pancreatectomy: an embryology-based resection. J Gastrointest Surg. 2006;10(3):434–438. – reference: 19) Tanaka M, Fernández-Del Castillo C, Kamisawa T, Jang JY, Levy P, Ohtsuka T, et al. Revisions of international consensus Fukuoka guidelines for the management of IPMN of the pancreas. Pancreatology. 2017;17:738–753. – reference: 15) Baiocco JA, Ackerman CT, Crawford JL, Yeo CJ. Intraductal papillary mucinous neoplasm and pancreas divisum: two cases. J Pancreat Cancer. 2016;2(1):28–31. – reference: 18) Ardengh JC, Taglieri E, Ardengh AO, De Almeida AF, Surjan RC, Makdissi F, et al. Intraoperative SpyGlass to determine extension of pancreatic resection in main duct intraductal papillary mucinous neoplasm associated with pancreas divisum. Endoscopy. 2021;53(5):E191–3. – reference: 6) Thayer SP, Fernández-del Castillo C, Balcom JH, Warshaw AL. Complete dorsal pancreatectomy with preservation of the ventral pancreas: a new surgical technique. Surgery. 2002;131(5):577–580. – reference: 22) 須藤 広誠,岡野 圭一,鈴木 康之.膵切除後の膵性糖尿病について.膵臓.2019;34(4):166–171. – reference: 24) 東原 琢,吉富 秀幸,清水 宏明,大塚 将之,加藤 厚,古川 勝規,ほか.中央区域温存膵切除術の4例.日本消化器外科学会雑誌.2016;49(5):439–446. – reference: 5) Warshaw AL, Simeone JF, Schapiro RH, Flavin-Warshaw B. Evaluation and treatment of the dominant dorsal duct syndrome (pancreas divisum redefined). Am J Surg. 1990;159(1):59–64; discussion -6. – reference: 2) Cotton PB. Congenital anomaly of pancreas divisum as cause of obstructive pain and pancreatitis. Gut. 1980;21(2):105–114. – reference: 10) Talbot ML, Foulis AK, Imrie CW. Total dorsal pancreatectomy for intraductal papillary mucinous neoplasm in a patient with pancreas divisum. Pancreatology. 2005;5(2–3):285–288. – reference: 13) Gurram KC, Czapla A, Thakkar S. Acute pancreatitis: pancreas divisum with ventral duct intraductal papillary mucinous neoplasms. BMJ Case Rep. 2014 Oct;2014:bcr2014205322. – reference: 3) 岡田 純,上坂 克彦,森本 剛史,小寺 泰弘,鳥井 彰人,平井 孝,ほか.膵管癒合不全の背側膵に発生した膵頭部癌の1例.日本消化器外科学会雑誌.1996;29(4):843–847. – reference: 14) Nishi T, Kawabata Y, Ishikawa N, Araki A, Yano S, Maruyama R, et al. Intraductal papillary mucinous carcinoma of the pancreas associated with pancreas divisum: a case report and review of the literature. BMC Gastroenterol. 2015;15:78. – reference: 8) Sakurai Y, Matsubara T, Imazu H, Hasegawa S, Miyakawa S, Ochiai M, et al. Intraductal papillary-mucinous tumor of the pancreas head with complete absence of the ventral pancreatic duct of Wirsung. J Hepatobiliary Pancreat Surg. 2004;11(4):293–298. – reference: 16) Di Mitri R, Scimeca D, Conte E, Unti E, Mocciaro F. Mixed-type intraductal papillary mucinous neoplasm in a patient with pancreas divisum: pancreatoscopy through the Santorini duct with direct intraductal biopsy. Gastrointest Endosc. 2020;91(6):1398–1400. – reference: 17) Dickson ZA, Sauer BG. Intraductal papillary mucinous neoplasm of the pancreas associated with pancreas divisum resulting in a “fish-eye” minor papilla. Gastrointest Endosc. 2020;91(6):1396–1397. – reference: 11) Akizuki E, Kimura Y, Mukaiya M, Honnma T, Koito K, Katsuramaki T, et al. A case of intraductal papillary mucinous tumor associated with pancreas divisum. Pancreas. 2006;32(1):117–118. – reference: 23) 村上 義昭,上村 健一郎,近藤 成,中川 直哉,岡野 圭介,岡田 健司郎,ほか.【膵内・外分泌機能をめぐる現状と展望】膵切除術における機能温存の考え方.膵臓.2017;32(4):706–713. – reference: 20) 竹山 宜典.【IPMN・MCN国際診療ガイドライン総まとめ】主膵管型IPMNの手術適応と術式.胆と膵.2020;41(1):37–40. – reference: 9) Sakate Y, Ohira M, Maeda K, Yamada N, Nishihara T, Nakata B, et al. Intraductal papillary-mucinous adenoma developed in the ventral pancreas in a patient with pancreas divisum. J Hepatobiliary Pancreat Surg. 2004;11(5):366–370. – reference: 21) 庭野 史丸,馬場谷 成,廣峰 義久,池上 博司.【膵全摘術を考える】膵全摘術後の膵内分泌機能異常(病態と治療).胆と膵.2019;40(1):75–79. |
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Snippet | 症例は74歳の女性で,膵炎の診断で前医入院加療された際に膵管内乳頭粘液性腫瘍(intraductal papillary mucinous... |
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SubjectTerms | 膵管内乳頭粘液性腫瘍 膵管癒合不全 |
Title | 膵管癒合不全に合併した膵管内乳頭粘液性腫瘍に対して尾側膵亜全摘を行った1例 |
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