急性硬膜外血腫(AEDH)を契機に発見された免疫性血小板減少症(ITP)の1例

AEDHを契機に発見されたITPの1例を経験したので報告する.症例は14歳男児,早産・低出生体重児であり二絨毛膜二羊膜双胎(DD twin)の第二子として出生した.けいれん,意識障害で受診しAEDHを認め開頭血腫除去術を施行した.術中の出血量は1,500 mlであったが明らかな骨折線や活動性の出血は認めなかった.術後経過は良好であった.血小板数の低値遷延から血液疾患の合併を疑い,精査した結果ITPの診断に至った....

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Published in小児の脳神経 Vol. 49; no. 4; pp. 189 - 193
Main Authors 小瀧, 祐, 矢尾板, 裕之, 齋藤, 太, 長野, 拓郎, 酒本, 海帆
Format Journal Article
LanguageJapanese
Published 一般社団法人 日本小児神経外科学会 2024
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ISSN0387-8023
2435-824X
DOI10.34544/jspn.49.4_189

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Abstract AEDHを契機に発見されたITPの1例を経験したので報告する.症例は14歳男児,早産・低出生体重児であり二絨毛膜二羊膜双胎(DD twin)の第二子として出生した.けいれん,意識障害で受診しAEDHを認め開頭血腫除去術を施行した.術中の出血量は1,500 mlであったが明らかな骨折線や活動性の出血は認めなかった.術後経過は良好であった.血小板数の低値遷延から血液疾患の合併を疑い,精査した結果ITPの診断に至った.
AbstractList AEDHを契機に発見されたITPの1例を経験したので報告する.症例は14歳男児,早産・低出生体重児であり二絨毛膜二羊膜双胎(DD twin)の第二子として出生した.けいれん,意識障害で受診しAEDHを認め開頭血腫除去術を施行した.術中の出血量は1,500 mlであったが明らかな骨折線や活動性の出血は認めなかった.術後経過は良好であった.血小板数の低値遷延から血液疾患の合併を疑い,精査した結果ITPの診断に至った.
Author 長野, 拓郎
矢尾板, 裕之
齋藤, 太
小瀧, 祐
酒本, 海帆
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References [2] Andoh S, Matsuura C, Sakaeyama Y, Okonogi S, Node Y, Masuda H, Kondo K, Harada N, Nemoto M, Sugo N: Acute contrecoup epidural hematoma that developed without skull fracture in two adults: two case reports. J Med Case Rep 12: 166, 2018.
[7] 早川勲 : 小児の頭部外傷.牧豊編 : 小児神経外科の進歩と展望.東京,にゅーろん社,1988, pp 33-41.
[1] Adolfo F, George R, Buchanan: Occult hemorrhage in children with severe ITP. Am J Hematol 91: 3, 2016.
[6] Hashimoto Y, Kajiwara S, Furuta K, Takeuchi Y, Morioka M: Pediatric acute epidural hematoma caused by contrecoup injury: illustrative case. J Neurosurg Case Lessons 3 (23), 2022.
[12] 酒井道生,藤沢康司,小原明,白幡聡 : 小児ITPとHelicobacter pylori.日小血会誌17: 413-417, 2003.
[5] Gallagher JP, Browder EJ: Extradural hematoma. Experience with 167 patients. J Neurosurg 29: 1-12, 1968.
[10] Mitsuyama T, Ide M, Kawamura H: Acute epidural hematoma caused by contrecoup head injury case report. BioMed Central 44: 584-586, 2004.
[3] Bullock MR, Chesnut R, Ghajar J, Gordon D, Hartl R, Newell DW, Servadei F, Walters BC, Wilberger JE: Surgical management of acute epidural hematomas. Neurosurgery 58: S7-15; discussion Si-iv, 2006.
[13] Zhang JY, Li Y, Ma YS, Sun XJ, Liu YZ, Yin YK, Hu B, Su MH, Li QL, Mi YC, et al: Clinical characteristics and prognostic factors in intracranial hemorrhage patients with hematological diseases. Ann Hematol 101: 2617-2625, 2022.
[9] Kelton JG, Powers PJ, Carter CJ: A prospective study of the usefulness of the measurement of platelet-associated IgG for the diagnosis of idiopathic thrombocytopenic purpura. Blood 60: 1050-1053, 1982.
[4] Fukai R, Takahashi K, Abe H, Higashiyama Y, Doi H, Takeuchi H, Tanaka F: Non-traumatic acute epidural hematoma in multiple sclerosis treated with fingolimod. Front Neurol 10: Article 763, 2019.
[8] 石黒精,森麻希子,宮川義隆,今泉益栄,小林尚明,笹原洋二,内山徹,野村理,堀内清華,高橋幸博,他 : 日本小児血液・がん学会2022年小児免疫性血小板減少症診療ガイドライン.The Japanese Journal of Pediatric Hematology/Oncology 59: 50-57, 2022.
[11] Neunert CE, Buchanan GR, Imbach P, Bolton-Maggs PH, Bennett CM, Neufeld EJ, Vesely SK, Adix L, Blanchette VS, Kühne T: Severe hemorrhage in children with newly diagnosed immune thrombocytopenic purpura. Blood 112: 4003-4008, 2008.
References_xml – reference: [1] Adolfo F, George R, Buchanan: Occult hemorrhage in children with severe ITP. Am J Hematol 91: 3, 2016.
– reference: [9] Kelton JG, Powers PJ, Carter CJ: A prospective study of the usefulness of the measurement of platelet-associated IgG for the diagnosis of idiopathic thrombocytopenic purpura. Blood 60: 1050-1053, 1982.
– reference: [7] 早川勲 : 小児の頭部外傷.牧豊編 : 小児神経外科の進歩と展望.東京,にゅーろん社,1988, pp 33-41.
– reference: [10] Mitsuyama T, Ide M, Kawamura H: Acute epidural hematoma caused by contrecoup head injury case report. BioMed Central 44: 584-586, 2004.
– reference: [8] 石黒精,森麻希子,宮川義隆,今泉益栄,小林尚明,笹原洋二,内山徹,野村理,堀内清華,高橋幸博,他 : 日本小児血液・がん学会2022年小児免疫性血小板減少症診療ガイドライン.The Japanese Journal of Pediatric Hematology/Oncology 59: 50-57, 2022.
– reference: [2] Andoh S, Matsuura C, Sakaeyama Y, Okonogi S, Node Y, Masuda H, Kondo K, Harada N, Nemoto M, Sugo N: Acute contrecoup epidural hematoma that developed without skull fracture in two adults: two case reports. J Med Case Rep 12: 166, 2018.
– reference: [12] 酒井道生,藤沢康司,小原明,白幡聡 : 小児ITPとHelicobacter pylori.日小血会誌17: 413-417, 2003.
– reference: [13] Zhang JY, Li Y, Ma YS, Sun XJ, Liu YZ, Yin YK, Hu B, Su MH, Li QL, Mi YC, et al: Clinical characteristics and prognostic factors in intracranial hemorrhage patients with hematological diseases. Ann Hematol 101: 2617-2625, 2022.
– reference: [6] Hashimoto Y, Kajiwara S, Furuta K, Takeuchi Y, Morioka M: Pediatric acute epidural hematoma caused by contrecoup injury: illustrative case. J Neurosurg Case Lessons 3 (23), 2022.
– reference: [5] Gallagher JP, Browder EJ: Extradural hematoma. Experience with 167 patients. J Neurosurg 29: 1-12, 1968.
– reference: [11] Neunert CE, Buchanan GR, Imbach P, Bolton-Maggs PH, Bennett CM, Neufeld EJ, Vesely SK, Adix L, Blanchette VS, Kühne T: Severe hemorrhage in children with newly diagnosed immune thrombocytopenic purpura. Blood 112: 4003-4008, 2008.
– reference: [4] Fukai R, Takahashi K, Abe H, Higashiyama Y, Doi H, Takeuchi H, Tanaka F: Non-traumatic acute epidural hematoma in multiple sclerosis treated with fingolimod. Front Neurol 10: Article 763, 2019.
– reference: [3] Bullock MR, Chesnut R, Ghajar J, Gordon D, Hartl R, Newell DW, Servadei F, Walters BC, Wilberger JE: Surgical management of acute epidural hematomas. Neurosurgery 58: S7-15; discussion Si-iv, 2006.
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Snippet AEDHを契機に発見されたITPの1例を経験したので報告する.症例は14歳男児,早産・低出生体重児であり二絨毛膜二羊膜双胎(DD twin)の第二子として出生した.けいれん,意識障害で受診しAEDHを認め開頭血腫除去術を施行した.術中の出血量は1,500...
SourceID jstage
SourceType Publisher
StartPage 189
SubjectTerms acute epidural hematoma
helicobacter pylori
hematological diseases
immune thrombocytopenia
pediatric
Title 急性硬膜外血腫(AEDH)を契機に発見された免疫性血小板減少症(ITP)の1例
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