Clear Cell Sarcoma of the Ileum: A Case Report
We report a case of clear cell sarcoma of the ileum in an adult. A 41-year-old woman presented with fever, hematochezia and anemia. A tumor in the pelvic cavity was visualized by abdominal CT and MRI. A segmental small bowel resection and sigmoidectomy were performed. Histological examination of the...
Saved in:
Published in | The Japanese Journal of Gastroenterological Surgery Vol. 49; no. 1; pp. 29 - 35 |
---|---|
Main Authors | , , , , , , , , , |
Format | Journal Article |
Language | Japanese |
Published |
The Japanese Society of Gastroenterological Surgery
01.01.2016
|
Subjects | |
Online Access | Get full text |
Cover
Loading…
Summary: | We report a case of clear cell sarcoma of the ileum in an adult. A 41-year-old woman presented with fever, hematochezia and anemia. A tumor in the pelvic cavity was visualized by abdominal CT and MRI. A segmental small bowel resection and sigmoidectomy were performed. Histological examination of the specimen revealed a tumor with epithelioid neoplasm which was infiltrating the bowel wall in sheets. The tumor cells had high nuclear-cytoplasmic ratio, and clear cytoplasm. The immunohistochemical profile of the tumor was focally positive for S-100, and diffusely positive for SOX10. EWRS1 gene rearrangement was observed during cytogenetic analysis. We diagnosed the tumor as a clear cell sarcoma of the ileum. The patient had postoperative adjuvant chemotherapy using doxorubicin and ifosfamide for five courses. No recurrences had observed for 28 months. |
---|---|
ISSN: | 0386-9768 1348-9372 |
DOI: | 10.5833/jjgs.2014.0247 |