Pediatrics Ewing's sarcoma of the sinonasal tract

Abstract Ewing's sarcoma (ES) is a highly malignant, small, round cell tumor that originates from the primitive neuroectodermal cells. Primary ES commonly occurs in early childhood or adolescence. It may present with skeletal and extraskeletal forms. The extraskeletal form is rarely encountered...

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Bibliographic Details
Published inJournal of pediatric surgery case reports
Main Authors Aldandan, Ahmed, Almomen, Ali, Alkhatib, Abdulrahman, Alazzeh, Ghaleb
Format Journal Article
LanguageEnglish
Published Elsevier Inc 2018
Subjects
Ewing's sarcoma
Extraskeletal
Head and neck ES
Sinonasal ES
Sinonasal tract
Surgery
Head and neck ES
Sinonasal tract
Ewing's sarcoma
Sinonasal ES
Extraskeletal
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Summary:Abstract Ewing's sarcoma (ES) is a highly malignant, small, round cell tumor that originates from the primitive neuroectodermal cells. Primary ES commonly occurs in early childhood or adolescence. It may present with skeletal and extraskeletal forms. The extraskeletal form is rarely encountered in the head and neck region and is extremely rare in the sinonasal tract. This is a case report of sinonasal ES in a 13-years old female patient who presented with a 7-months history of right nasal obstruction, anosmia, intermittent epistaxis, snoring and hearing loss. Clinical examination revealed a right nasal mass pushing the septum to the left side and extending to the nasopharynx. Endoscopic biopsy and histopathological analysis showed a small blue cell tumor suggestive of ES. The patient was treated with surgery, radiotherapy and chemotherapy. After a follow-up of 5 years, the patient remains recurrence-free with excellent functional status and quality of life.
ISSN:2213-5766
2213-5766
DOI:10.1016/j.epsc.2018.12.023