Imaging signatures in diffuse choroidal hemangioma in a case of sturge weber syndrome

Sturge–Weber syndrome (SWS) is a rare congenital neurocutaneous disorder characterized by facial port-wine stain, leptomeningeal hemangiomas, and ocular manifestations such as glaucoma and diffuse choroidal hemangioma (DCH). DCH is a benign vascular lesion characteristically seen in up to 50% of pat...

Full description

Saved in:
Bibliographic Details
Published inIP International Journal of Ocular Oncology and Oculoplasty Vol. 9; no. 4; pp. 219 - 221
Main Authors Pandit, Rinal, Shah, Dhaivat, Agrawal, Deepanshu, Gorhe, Sukanya, Sharma, Neha
Format Journal Article
LanguageEnglish
Published 28.02.2024
Online AccessGet full text

Cover

More Information
Summary:Sturge–Weber syndrome (SWS) is a rare congenital neurocutaneous disorder characterized by facial port-wine stain, leptomeningeal hemangiomas, and ocular manifestations such as glaucoma and diffuse choroidal hemangioma (DCH). DCH is a benign vascular lesion characteristically seen in up to 50% of patients affected with SWS. Diffuse choroidal hemangioma can cause refractive error, foveal distortion, and exudative retinal detachment and contribute to vision loss. We report a case of a young male with SWS and a unilateral DCH with characteristic imaging features.
ISSN:2581-5024
2581-5016
DOI:10.18231/j.ijooo.2023.047