Crouzon Syndrome Associated with Congenital Coarctation of Aorta

• Published in: Chinese medical journal Vol. 131; no. 12; pp. 1498 - 1499
• Main Authors: Meng, Bing, Zhang, Hui
• Format: Journal Article
• Language: English
• Published: China Wolters Kluwer India Pvt. Ltd 20.06.2018; Medknow Publications and Media Pvt. Ltd; Lippincott Williams & Wilkins Ovid Technologies; Department of Cardiac Surgery, Children's Hospital Affiliated to the Capital Institute of Pediatrics, Beijing 100020, China; Medknow Publications & Media Pvt Ltd; Wolters Kluwer
• Subjects: Airway management; Aorta; Aorta, Thoracic; Aortic Coarctation - complications; Children & youth; Congenital diseases; Consent; Coronary vessels; Correspondence; Craniofacial Dysostosis - complications; Defects; Families & family life; Fibroblasts; Growth factors; Heart Defects, Congenital - complications; Heart surgery; Humans; Mutation; Neurosurgery; Pediatrics; Beijing China
• ISSN: 0366-6999; 2542-5641
• DOI: 10.4103/0366-6999.233963

Computed tomography scan of cardiac and main blood vessel showed that the proximal ascending aorta diameter was 12.2 mm, proximal aortic arch diameter was 5.5 mm, distal aortic arch was 3.5 mm, and the beyond left subclavian artery was 8.0 mm. Aortic isthmus was severely narrow, almost interrupted, beyond which the vascular cavity diameter was 10.7 mm [Figure 1]b. The repeated magnetic resonance imaging demonstrated a few other comorbidities such as on-progression hydrocephalus, cerebellar infratentorial herniation, posterior laryngeal wall stenosis, and severe obstructive sleep apnea [Figure 1]c. Thereby, a cranial decompression procedure was performed, followed by a combined elective surgery involving cardiac and neurological surgical units on December 6, 2017. [...]the patient was discharged 8 days postoperatively. [...]the combined surgical approach between cardiac surgery and neurosurgery was adopted to lower the perioperative risks and gain more time for advanced procedures.