Hybrid Repair for Mega-Aortic Syndrome due to Giant Cell Aortitis in a Heart Failure Patient

• Published in: Annals of Vascular Diseases Vol. 13; no. 1; pp. 76 - 80
• Main Authors: Inoue, Takehiro, Fujii, Kosuke, Kino, Shigeo, Yukami, Shintaro, Miyashita, Naoya, Kitayama, Hitoshi
• Format: Journal Article
• Language: English
• Published: Japan The Editorial Committee of Annals of Vascular Diseases 25.03.2020; Japanese College of Angiology / The Japanese Society for Vascular Surgery / Japanese Society of Phlebology
• Subjects: Case Report; giant cell aortitis; hybrid repair; mega-aortic syndrome; hybrid repair; mega-aortic syndrome; giant cell aortitis
• ISSN: 1881-641X; 1881-6428
• DOI: 10.3400/avd.cr.19-00096

The present report describes a case of mega-aortic syndrome accompanied with severe aortic regurgitation in a 75-year-old man who underwent a two-stage hybrid repair. Intraoperative pathologic findings at the first repair, consisting of Bentall operation and total arch replacement with a Lupiae graft, aided the identification of the giant cell aortitis. Despite complicating hemorrhagic stroke, steroid therapy was initiated and endovascular repair was subsequently completed. Over more than 2 years of follow-up, the patient continued steroid therapy and is doing well without any reintervention.