Implantation of a Left Ventricular Assist Device for Danon Cardiomyopathy

This is the first report of Danon cardiomyopathy managed with a left ventricular assist device (LVAD). Danon disease is an X-linked dominant inheritance disorder. Heart failure with Danon cardiomyopathy results in a poor prognosis, and heart transplantation is the treatment of choice. We present two...

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Published inThe Annals of thoracic surgery Vol. 103; no. 1; pp. e39 - e41
Main Authors Kitahara, Hiroto, MD, Nawata, Kan, MD, Kinoshita, Osamu, MD, Itoda, Yoshifumi, MD, Shintani, Yukako, MD, Fukayama, Masashi, MD, Ono, Minoru, MD
Format Journal Article
LanguageEnglish
Published Netherlands Elsevier Inc 2017
Subjects
Adult
Biopsy
Cardiac Surgical Procedures - methods
Cardiomyopathy, Hypertrophic - diagnosis
Cardiomyopathy, Hypertrophic - surgery
Cardiothoracic Surgery
Female
Heart-Assist Devices
Humans
Myocardium - pathology
Surgery
Young Adult
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Summary:This is the first report of Danon cardiomyopathy managed with a left ventricular assist device (LVAD). Danon disease is an X-linked dominant inheritance disorder. Heart failure with Danon cardiomyopathy results in a poor prognosis, and heart transplantation is the treatment of choice. We present two cases of successful implantation of an LVAD for Danon cardiomyopathy. Patient 1 was in the dilatated phase of hypertrophic cardiomyopathy (HCM) with Danon cardiomyopathy, and she underwent LVAD implantation. She is waiting for transplantation. Patient 2 had dilatated cardiomyopathy with Danon cardiomyopathy and received transplantation 990 days after LVAD implantation without myopathy or intellectual disability.
Bibliography:ObjectType-Case Study-2
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ISSN:0003-4975
1552-6259
DOI:10.1016/j.athoracsur.2016.07.022