Unilateral Nevoid Telangiectasia in a Healthy Man

We report the case of a healthy 26-year-old man presenting telangiectatic macules on the left thorax and arm since childhood. The main diagnostic hypothesis were unilateral nevoid telangiectasia (UNT), hereditary benign telangiectasia, atrial myxoma, segmental serpiginous angioma, circumscribed nevi...

Full description

Saved in:
Bibliographic Details
Published inCase reports in dermatology Vol. 13; no. 2; pp. 330 - 335
Main Authors Küçük, Kirley, Bourlond, Florence, Votquenne, Nicolas, Benhadou, Farida
Format Journal Article
LanguageEnglish
Published Basel, Switzerland S. Karger AG 23.06.2021
Karger Publishers
Subjects
Asymptomatic
Case reports
Congenital diseases
dermatomes
Estrogens
hyperestrogenism
Literature reviews
liver disorder
Men
Mens health
myxoma
Pregnancy
Puberty
Single Case
Thorax
Ultrasonic imaging
unilateral nevoid telangiectasia
Dermatomes
Hyperestrogenism
Myxoma
Unilateral nevoid telangiectasia
Liver disorder
Online AccessGet full text

Cover

More Information
Summary:We report the case of a healthy 26-year-old man presenting telangiectatic macules on the left thorax and arm since childhood. The main diagnostic hypothesis were unilateral nevoid telangiectasia (UNT), hereditary benign telangiectasia, atrial myxoma, segmental serpiginous angioma, circumscribed neviform angiokeratoma, and nevus vascularis mixtus. The diagnosis retained was UNT characterized by congenital or acquired telangiectasia distributed asymmetrically along the upper extremities, or the third or fourth cervical dermatomes. The congenital form is extremely rare, predominant in men, and persists in adulthood. The acquired form is most frequent, affects preferentially women, usually appears at puberty or during pregnancy and tends to disappear. Estrogen excess triggers the formation of telangiectasia. UNT is rarely associated with liver or thyroid disorder. Pulsed-dye lasers and normalization of estrogen are proposed as therapeutic options. We report a rare diagnosis of UNT in a young man with no other underlying condition. We would like to highlight that in the presence of unilateral telangiectasia, a complete clinical examination must be performed to rule out signs of hyperestrogenism in man, ocular or neurological abnormalities, a blood test to exclude pregnancy, hepatic and thyroid dysfunctions, and ultrasonography in case of suspicion of atrial myxoma.
ISSN:1662-6567
1662-6567
DOI:10.1159/000514941