An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization Lab

The association of pulmonary atresia, ventricular septal defect (VSD) and major aortopulmonary collaterals (MAPCA) is an extreme form of tetralogy of Fallot (TOF). It carries a high mortality risk if not intervened on during infancy with only 20% of unoperated patients surviving into adulthood. We p...

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Bibliographic Details
Published inCase Reports in Cardiology Vol. 2020; no. 2020; pp. 1 - 3
Main Authors Smalling, Richard W., Tung, Poyee, Walton, Brian, Bravo-Jaimes, Katia
Format Journal Article
LanguageEnglish
Published Cairo, Egypt Hindawi Publishing Corporation 27.01.2020
Hindawi
John Wiley & Sons, Inc
Hindawi Limited
Subjects
Adults
Cardiac catheterization
Cardiovascular disease
Case Report
Case reports
Congenital diseases
Congenital heart disease
Coronary vessels
Defects
Health aspects
Heart
Intubation
Mortality
Patients
Pulmonary arteries
Surgery
Thoracic surgery
Ultrasonic imaging
Veins & arteries
United States > US
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Summary:The association of pulmonary atresia, ventricular septal defect (VSD) and major aortopulmonary collaterals (MAPCA) is an extreme form of tetralogy of Fallot (TOF). It carries a high mortality risk if not intervened on during infancy with only 20% of unoperated patients surviving into adulthood. We present the case of a 40-year-old man who presented for evaluation prior to retinal surgery and was found to have hypoxia and a loud murmur. Cardiac catheterization was performed in the general catheterization laboratory, demonstrating a membranous VSD, pulmonary atresia, and MAPCA. We highlight the challenges and limitations that an adult interventional cardiologist may have when encountering these patients.
Bibliography:Academic Editor: Ertugrul Ercan
ISSN:2090-6404
2090-6412
DOI:10.1155/2020/4726529